{"orpha":730276,"name":"Primary autoimmune ear disease","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Primary autoimmune sensorineural hearing loss","Immune mediated inner ear disease type 1","IMIED type 1"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-730276/","orphanet_url":"https://www.orpha.net/en/disease/detail/730276","names":{"fr":{"name":"Maladie auto-immune de l'oreille interne","synonyms":["Perte auditive neurosensorielle auto-immune primaire","MAOI primaire"]},"de":{"name":"Primäre Autoimmunerkrankungen des Innenohres","synonyms":["IMIED Typ 1","Immunvermittelte Innenohrerkrankung Typ 1","Primärer autoimmuner sensorineuraler Hörverlust"]},"es":{"name":"Enfermedad autoinmune primaria del oído","synonyms":["Enfermedad inmunomediada del oído interno tipo 1","Hipoacusia neurosensorial autoinmune primaria","IMIED tipo 1"]},"it":{"name":"Malattia autoimmune primitiva dell'orecchio","synonyms":["IMIED tipo 1","Malattia dell'orecchio interno immuno-mediata tipo 1","Sordità neurosensoriale autoimmune primitiva"]},"nl":{"name":"Primaire auto-immune oorziekte","synonyms":["IMIED type 1","Immuungemedieerde aandoening van binnenoor type 1","Primair auto-immuun sensorineuraal gehoorverlies"]},"pt":{"name":"Primary autoimmune ear disease"},"pl":{"name":"Primary autoimmune ear disease","synonyms":["Primary autoimmune sensorineural hearing loss","Immune mediated inner ear disease type 1","IMIED type 1"]},"cs":{"name":"Primary autoimmune ear disease","synonyms":["Primary autoimmune sensorineural hearing loss","Immune mediated inner ear disease type 1","IMIED type 1"]}},"xrefs":[],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98036,"name":"Rare otorhinolaryngologic disease"},"parents":[{"orpha":68361,"name":"Rare deafness","classifications":[200]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}