raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:728633

Idiopathic orbital inflammation syndrome

Synonyms: Orbital pseudotumor · Orbital inflammatory pseudotumor · OIP · IOI syndrome · Syndrome IOI

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult, Childhood, Elderly
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enIdiopathic orbital inflammation syndromeOrbital pseudotumor · Orbital inflammatory pseudotumor · OIP · IOI syndrome · Syndrome IOI
frSyndrome d'inflammation de l'orbite idiopathiquePseudotumeur inflammatoire orbitaire
deIdiopathisches orbitales EntzündungssyndromIdiopathische Orbitaentzündung · IOE · IOI-Syndrom · Idiopathische entzündliche Orbitopathie
esSíndrome de inflamación orbitaria idiopáticaPIO · Pseudotumor inflamatorio orbitario · Pseudotumor orbitario · Síndrome IOI
itSindrome infiammatoria idiopatica dell'orbitaOIP · Sindrome IOI · Pseudotumore dell'orbita · Pseudotumore infiammatorio dell'orbita
nlIdiopathische inflammatie van orbitaInflammatoire pseudotumor van orbita · Pseudotumor van orbita · IOI-syndroom · OIP
ptIdiopathic orbital inflammation syndrome
plIdiopathic orbital inflammation syndrome= en
csIdiopathic orbital inflammation syndrome= en
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card