{"orpha":728633,"name":"Idiopathic orbital inflammation syndrome","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Orbital pseudotumor","Orbital inflammatory pseudotumor","OIP","IOI syndrome","Syndrome IOI"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-728633/","orphanet_url":"https://www.orpha.net/en/disease/detail/728633","names":{"fr":{"name":"Syndrome d'inflammation de l'orbite idiopathique","synonyms":["Pseudotumeur inflammatoire orbitaire"]},"de":{"name":"Idiopathisches orbitales Entzündungssyndrom","synonyms":["Idiopathische Orbitaentzündung","IOE","IOI-Syndrom","Idiopathische entzündliche Orbitopathie"]},"es":{"name":"Síndrome de inflamación orbitaria idiopática","synonyms":["PIO","Pseudotumor inflamatorio orbitario","Pseudotumor orbitario","Síndrome IOI"]},"it":{"name":"Sindrome infiammatoria idiopatica dell'orbita","synonyms":["OIP","Sindrome IOI","Pseudotumore dell'orbita","Pseudotumore infiammatorio dell'orbita"]},"nl":{"name":"Idiopathische inflammatie van orbita","synonyms":["Inflammatoire pseudotumor van orbita","Pseudotumor van orbita","IOI-syndroom","OIP"]},"pt":{"name":"Idiopathic orbital inflammation syndrome"},"pl":{"name":"Idiopathic orbital inflammation syndrome","synonyms":["Orbital pseudotumor","Orbital inflammatory pseudotumor","OIP","IOI syndrome","Syndrome IOI"]},"cs":{"name":"Idiopathic orbital inflammation syndrome","synonyms":["Orbital pseudotumor","Orbital inflammatory pseudotumor","OIP","IOI syndrome","Syndrome IOI"]}},"xrefs":[],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97966,"name":"Rare ophthalmic disorder"},"parents":[{"orpha":519329,"name":"Rare disorder involving multiple structures of the eye","classifications":[189]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult","Childhood","Elderly"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}