raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:725992

High-grade appendiceal mucinous neoplasm

Synonyms: HAMN · High-grade mucinous neoplasm of the appendix

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enHigh-grade appendiceal mucinous neoplasmHAMN · High-grade mucinous neoplasm of the appendix
frTumeur appendiculaire mucineuse de haut gradeHAMN · Tumeur mucineuse de l'appendice de haut grade
deHochgradige muzinöse Neoplasie der AppendixHAMN · Muzinöse Appendixneoplasie, hochgradige
esNeoplasia mucinosa apendicular de alto gradoNeoplasia mucinosa de alto grado del apéndice
itNeoplasia mucinosa appendicolare di alto gradoHAMN · Neoplasia mucinosa dell’appendice di alto grado
nlHooggradig appendiculair mucineus neoplasmaHAMN · Hooggradig mucineus neoplasma van appendix
ptHigh-grade mucinous neoplasm
plHigh-grade appendiceal mucinous neoplasm= en
csHigh-grade appendiceal mucinous neoplasm= en
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card