ORPHA:725964
Appendiceal mucinous neoplasm
Synonyms: AMN · Mucinious neoplasm of the appendix
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
Orphadata ships no English definition for this code.
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Names in Orphadata languages
9 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Appendiceal mucinous neoplasm | AMN · Mucinious neoplasm of the appendix |
| fr | Tumeur appendiculaire mucineuse | AMN · Tumeur mucineuse de l'appendice |
| de | Muzinöse Neoplasie der Appendix | AMN · Appendixneoplasie, muzinöse |
| es | Neoplasia mucinosa apendicular | Neoplasia mucinosa del apéndice |
| it | Neoplasia mucinosa appendicolare | AMN · Neoplasia mucinosa dellappendice |
| nl | Appendiculair mucineus neoplasma | AMN · Mucineus neoplasma van appendix |
| pt | Appendiceal mucinous neoplasm | |
| pl | Appendiceal mucinous neoplasm | = en |
| cs | Appendiceal mucinous neoplasm | = en |
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Cross-references
qualifier = Orphanet mapping relationNo cross-references in this release.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:423982Epithelial tumor of the appendix
rare gastroenterological diseases; rare neoplastic diseases; rare transplant-related disorders
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 1 000 000 | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/725964
- This record as JSON: /data/d/725964.json