raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:699702

Necrotizing myositis

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
Adult, Elderly
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enNecrotizing myositis
frMyosite nécrosante
deNekrotisierende Myositis
esMiositis necrosante
itMiosite necrotizzante
nlNecrotiserende myositis
ptNecrotizing myositis
plNecrotizing myositis
csNecrotizing myositis
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalence1-9 / 100 000—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card