ORPHA:698059
Fibromuscular dysplasia of the coronary arteries
Synonyms: Epicardial coronary artery fibromuscular dysplasia
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
Orphadata ships no English definition for this code.
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Names in Orphadata languages
9 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Fibromuscular dysplasia of the coronary arteries | Epicardial coronary artery fibromuscular dysplasia |
| fr | Dysplasie fibromusculaire des artères coronaires | |
| de | Fibromuskuläre Dysplasie der Koronararterien | |
| es | Displasia fibromuscular de las arterias coronarias | Displasia fibromuscular de la arteria coronaria epicárdica |
| it | Displasia fibromuscolare delle arterie coronarie | Displasia fibromuscolare delle arterie coronarie epicardiche |
| nl | Fibromusculaire dysplasie van kransslagaders | Fibromusculaire dysplasie van epicardiale kransslagaders |
| pt | Fibromuscular dysplasia of the coronary arteries | |
| pl | Fibromuscular dysplasia of the coronary arteries | = en |
| cs | Fibromuscular dysplasia of the coronary arteries | = en |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | I77.3 | NTBT | attributed | not yet validated |
| ICD-11 | BD41.0 | NTBT | attributed | not yet validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:698012Fibromuscular dysplasia
rare circulatory system diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | 1-5 / 10 000 | 27 / 100 000 | Worldwide | Value and class | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/698059
- This record as JSON: /data/d/698059.json