{"orpha":698059,"name":"Fibromuscular dysplasia of the coronary arteries","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Epicardial coronary artery fibromuscular dysplasia"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-698059/","orphanet_url":"https://www.orpha.net/en/disease/detail/698059","names":{"fr":{"name":"Dysplasie fibromusculaire des artères coronaires"},"de":{"name":"Fibromuskuläre Dysplasie der Koronararterien"},"es":{"name":"Displasia fibromuscular de las arterias coronarias","synonyms":["Displasia fibromuscular de la arteria coronaria epicárdica"]},"it":{"name":"Displasia fibromuscolare delle arterie coronarie","synonyms":["Displasia fibromuscolare delle arterie coronarie epicardiche"]},"nl":{"name":"Fibromusculaire dysplasie van kransslagaders","synonyms":["Fibromusculaire dysplasie van epicardiale kransslagaders"]},"pt":{"name":"Fibromuscular dysplasia of the coronary arteries"},"pl":{"name":"Fibromuscular dysplasia of the coronary arteries","synonyms":["Epicardial coronary artery fibromuscular dysplasia"]},"cs":{"name":"Fibromuscular dysplasia of the coronary arteries","synonyms":["Epicardial coronary artery fibromuscular dysplasia"]}},"xrefs":[{"source":"ICD-10","code":"I77.3","qualifier":"NTBT","icd_relation":"attributed","validated":false},{"source":"ICD-11","code":"BD41.0","qualifier":"NTBT","icd_relation":"attributed","validated":false}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98028,"name":"Rare circulatory system disease"},"parents":[{"orpha":698012,"name":"Fibromuscular dysplasia","classifications":[198]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult","Elderly"],"prevalence":[{"type":"Point prevalence","qualification":"Value and class","class":"1-5 / 10 000","value":27.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}