ORPHA:698043
Fibromuscular dysplasia of the renal arteries
Synonyms: Renal FMD · Renal artery fibromuscular dysplasia
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
Orphadata ships no English definition for this code.
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Names in Orphadata languages
9 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Fibromuscular dysplasia of the renal arteries | Renal FMD · Renal artery fibromuscular dysplasia |
| fr | Dysplasie fibromusculaire des artères rénales | DFM rénale · Dysplasie fibromusculaire rénale |
| de | Fibromuskuläre Dysplasie der Nierenarterien | Renale FMD |
| es | Displasia fibromuscular de las arterias renales | DFM renal |
| it | Displasia fibromuscolare delle arterie renali | FMD renale · Displasia fibromuscolare delle arterie renali |
| nl | Fibromusculaire dysplasie van nierarteriën | Renale FMD |
| pt | Fibromuscular dysplasia of the renal arteries | |
| pl | Fibromuscular dysplasia of the renal arteries | = en |
| cs | Fibromuscular dysplasia of the renal arteries | = en |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | I77.3 | NTBT | attributed | not yet validated |
| ICD-11 | BD41.0 | NTBT | index | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:698012Fibromuscular dysplasia
rare circulatory system diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/698043
- This record as JSON: /data/d/698043.json