raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:698043

Fibromuscular dysplasia of the renal arteries

Synonyms: Renal FMD · Renal artery fibromuscular dysplasia

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enFibromuscular dysplasia of the renal arteriesRenal FMD · Renal artery fibromuscular dysplasia
frDysplasie fibromusculaire des artères rénalesDFM rénale · Dysplasie fibromusculaire rénale
deFibromuskuläre Dysplasie der NierenarterienRenale FMD
esDisplasia fibromuscular de las arterias renalesDFM renal
itDisplasia fibromuscolare delle arterie renaliFMD renale · Displasia fibromuscolare delle arterie renali
nlFibromusculaire dysplasie van nierarteriënRenale FMD
ptFibromuscular dysplasia of the renal arteries
plFibromuscular dysplasia of the renal arteries= en
csFibromuscular dysplasia of the renal arteries= en
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10I77.3NTBTattributednot yet validated
ICD-11BD41.0NTBTindexvalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card