{"orpha":698043,"name":"Fibromuscular dysplasia of the renal arteries","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Renal FMD","Renal artery fibromuscular dysplasia"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-698043/","orphanet_url":"https://www.orpha.net/en/disease/detail/698043","names":{"fr":{"name":"Dysplasie fibromusculaire des artères rénales","synonyms":["DFM rénale","Dysplasie fibromusculaire rénale"]},"de":{"name":"Fibromuskuläre Dysplasie der Nierenarterien","synonyms":["Renale FMD"]},"es":{"name":"Displasia fibromuscular de las arterias renales","synonyms":["DFM renal"]},"it":{"name":"Displasia fibromuscolare delle arterie renali","synonyms":["FMD renale","Displasia fibromuscolare delle arterie renali"]},"nl":{"name":"Fibromusculaire dysplasie van nierarteriën","synonyms":["Renale FMD"]},"pt":{"name":"Fibromuscular dysplasia of the renal arteries"},"pl":{"name":"Fibromuscular dysplasia of the renal arteries","synonyms":["Renal FMD","Renal artery fibromuscular dysplasia"]},"cs":{"name":"Fibromuscular dysplasia of the renal arteries","synonyms":["Renal FMD","Renal artery fibromuscular dysplasia"]}},"xrefs":[{"source":"ICD-10","code":"I77.3","qualifier":"NTBT","icd_relation":"attributed","validated":false},{"source":"ICD-11","code":"BD41.0","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1177091716"}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98028,"name":"Rare circulatory system disease"},"parents":[{"orpha":698012,"name":"Fibromuscular dysplasia","classifications":[198]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}