ORPHA:696175
Encapsulating peritoneal sclerosis
Synonyms: Abdominal cocoon syndrome · EPS · Sclerosing encapsulating peritonitis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
Orphadata ships no English definition for this code.
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Names in Orphadata languages
9 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Encapsulating peritoneal sclerosis | Abdominal cocoon syndrome · EPS · Sclerosing encapsulating peritonitis |
| fr | Péritonite encapsulante sclérosante | Abdominal cocoon syndrome · PSE |
| de | Peritonealsklerose, verkapselte | Abdominelles Cocoon-Syndrom · EPS · Sklerosierende kapselbildende Peritonitis |
| es | Esclerosis peritoneal encapsulante | Peritonitis esclerosante encapsulada · SEP · Síndrome del capullo abdominal |
| it | Sclerosi peritoneale incapsulante | Sindrome del bozzolo addominale · EPS · Peritonite sclerosante incapsulante |
| nl | Encapsulerende peritoneale sclerose | Abdominaal inkapselingssyndroom · EPS · Scleroserende encapsulerende peritonitis |
| pt | Encapsulating peritoneal sclerosis | |
| pl | Encapsulating peritoneal sclerosis | = en |
| cs | Encapsulating peritoneal sclerosis | = en |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | K66.8 | NTBT | attributed | validated |
| ICD-11 | DC50.12 | NTBT | index | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:165711Rare abdominal surgical disease
rare abdominal surgical diseases - ORPHA:97935Rare gastroenterologic disease
rare gastroenterological diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | <1 / 1 000 000 | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/696175
- This record as JSON: /data/d/696175.json