{"orpha":696175,"name":"Encapsulating peritoneal sclerosis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Abdominal cocoon syndrome","EPS","Sclerosing encapsulating peritonitis"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-696175/","orphanet_url":"https://www.orpha.net/en/disease/detail/696175","names":{"fr":{"name":"Péritonite encapsulante sclérosante","synonyms":["Abdominal cocoon syndrome","PSE"]},"de":{"name":"Peritonealsklerose, verkapselte","synonyms":["Abdominelles Cocoon-Syndrom","EPS","Sklerosierende kapselbildende Peritonitis"]},"es":{"name":"Esclerosis peritoneal encapsulante","synonyms":["Peritonitis esclerosante encapsulada","SEP","Síndrome del capullo abdominal"]},"it":{"name":"Sclerosi peritoneale incapsulante","synonyms":["Sindrome del bozzolo addominale","EPS","Peritonite sclerosante incapsulante"]},"nl":{"name":"Encapsulerende peritoneale sclerose","synonyms":["Abdominaal inkapselingssyndroom","EPS","Scleroserende encapsulerende peritonitis"]},"pt":{"name":"Encapsulating peritoneal sclerosis"},"pl":{"name":"Encapsulating peritoneal sclerosis","synonyms":["Abdominal cocoon syndrome","EPS","Sclerosing encapsulating peritonitis"]},"cs":{"name":"Encapsulating peritoneal sclerosis","synonyms":["Abdominal cocoon syndrome","EPS","Sclerosing encapsulating peritonitis"]}},"xrefs":[{"source":"ICD-10","code":"K66.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"DC50.12","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1269928839"}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":165711,"name":"Rare abdominal surgical disease"},"parents":[{"orpha":165711,"name":"Rare abdominal surgical disease","classifications":[182]},{"orpha":97935,"name":"Rare gastroenterologic disease","classifications":[152]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}