ORPHA:695631
Primary vitreoretinal large B-cell lymphoma
Synonyms: PVLR · PVR-LBCL · Primary diffuse large B-cell lymphoma of the virtreoretina
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
Orphadata ships no English definition for this code.
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Names in Orphadata languages
9 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary vitreoretinal large B-cell lymphoma | PVLR · PVR-LBCL · Primary diffuse large B-cell lymphoma of the virtreoretina |
| fr | Lymphome vitréorétinien primitif à grandes cellules B | LVRP · Lymphome diffus primaire à grandes cellules B vitréorétinien |
| de | Primäres vitreoretinales großzelliges B-Zell-Lymphom | PVLR · PVR-LBCL · Primäres diffuses großzelliges B-Zell-Lymphom der Vitreoretina |
| es | Linfoma vitreorretiniano primario de células B grandes | Linfoma vitreorretiniano primario difuso de células B grandes · PVLR · PVR-LBCL |
| it | Linfoma vitreoretinico primitivo a grandi cellule B | PVLR · PVR-LBCL · Linfoma primitivo diffuso a grandi cellule B della vitreoretina |
| nl | Primair vitreoretinaal grootcellig B-cellymfoom | PVLR · PVR-LBCL · Primair diffuus vitreoretinaal grootcellig B-cellymfoom |
| pt | Primary vitreoretinal large B-cell lymphoma | |
| pl | Primary vitreoretinal large B-cell lymphoma | = en |
| cs | Primary vitreoretinal large B-cell lymphoma | = en |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C85.7 | NTBT | attributed | validated |
| ICD-11 | 2B33.5 | NTBT | index | validated |
| MONDO | 4351 | E | validated | |
| MeSH | D064090 | E | validated | |
| UMLS | C0281658 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:544Diffuse large B-cell lymphoma
rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders - ORPHA:730376Rare acquired isolated progressive generalized retinal disorder
rare ophthalmic disorders
No children.
Codes that Orphanet moved or referred to this one:
- ORPHA:279904OBSOLETE: Primary intraocular lymphoma referred to · inactive
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | <1 / 1 000 000 | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/695631
- This record as JSON: /data/d/695631.json