{"orpha":695631,"name":"Primary vitreoretinal large B-cell lymphoma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["PVLR","PVR-LBCL","Primary diffuse large B-cell lymphoma of the virtreoretina"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-695631/","orphanet_url":"https://www.orpha.net/en/disease/detail/695631","names":{"fr":{"name":"Lymphome vitréorétinien primitif à grandes cellules B","synonyms":["LVRP","Lymphome diffus primaire à grandes cellules B vitréorétinien"]},"de":{"name":"Primäres vitreoretinales großzelliges B-Zell-Lymphom","synonyms":["PVLR","PVR-LBCL","Primäres diffuses großzelliges B-Zell-Lymphom der Vitreoretina"]},"es":{"name":"Linfoma vitreorretiniano primario de células B grandes","synonyms":["Linfoma vitreorretiniano primario difuso de células B grandes","PVLR","PVR-LBCL"]},"it":{"name":"Linfoma vitreoretinico primitivo a grandi cellule B","synonyms":["PVLR","PVR-LBCL","Linfoma primitivo diffuso a grandi cellule B della vitreoretina"]},"nl":{"name":"Primair vitreoretinaal grootcellig B-cellymfoom","synonyms":["PVLR","PVR-LBCL","Primair diffuus vitreoretinaal grootcellig B-cellymfoom"]},"pt":{"name":"Primary vitreoretinal large B-cell lymphoma"},"pl":{"name":"Primary vitreoretinal large B-cell lymphoma","synonyms":["PVLR","PVR-LBCL","Primary diffuse large B-cell lymphoma of the virtreoretina"]},"cs":{"name":"Primary vitreoretinal large B-cell lymphoma","synonyms":["PVLR","PVR-LBCL","Primary diffuse large B-cell lymphoma of the virtreoretina"]}},"xrefs":[{"source":"ICD-10","code":"C85.7","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2B33.5","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"959217874"},{"source":"MONDO","code":"4351","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D064090","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0281658","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[{"type":"Referred to","orpha":279904,"name":"OBSOLETE: Primary intraocular lymphoma","status":"inactive"}],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":544,"name":"Diffuse large B-cell lymphoma","classifications":[194,202,233]},{"orpha":730376,"name":"Rare acquired isolated progressive generalized retinal disorder","classifications":[189]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult","Elderly"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}