ORPHA:695131
Acinar cystic transformation of the pancreas
Synonyms: Acinar cell cystadnoma · Pancreatic acinar cystic transformation
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adolescent, Adult, Childhood, Elderly
- Status
- active
Orphadata ships no English definition for this code.
1
Names in Orphadata languages
9 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Acinar cystic transformation of the pancreas | Acinar cell cystadnoma · Pancreatic acinar cystic transformation |
| fr | Transformation kystique des acini du pancréas | Transformation kystique des acini pancréatiques · TKA pancréatique |
| de | Azinäre zystische Transformation des Pankreas | Azinuszell-Zystadenom des Pankreas · Pankreatische akinäre zystische Transformation |
| es | Transformación quística acinar del páncreas | Cistoadenoma de células acinares · Transformación quística acinar pancreática |
| it | Trasformazione cistica acinare del pancreas | Trasformazione cistica degli acini pancreatici · Cistadenoma a cellule acinari · Trasformazione cistica acinare del pancreas |
| nl | Acinaire cystische transformatie van pancreas | Acinaire cystische transformatie van alvleesklier · Acinuscelcystadenoom |
| pt | Acinar cystic transformation of the pancreas | |
| pl | Zrazikowo-torbielowata transformacja trzustki | = en |
| cs | Acinar cystic transformation of the pancreas | = en |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D13.6 | NTBT | attributed | validated |
| ICD-11 | 2E92.8 | NTBT | index | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:101937Rare pancreatic disease
rare gastroenterological diseases
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Cases/families | 50 cases | Worldwide | Case(s) | Validated | ORPHANET | |
| Point prevalence | <1 / 1 000 000 | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/695131
- This record as JSON: /data/d/695131.json