{"orpha":695131,"name":"Acinar cystic transformation of the pancreas","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Acinar cell cystadnoma","Pancreatic acinar cystic transformation"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-695131/","orphanet_url":"https://www.orpha.net/en/disease/detail/695131","names":{"fr":{"name":"Transformation kystique des acini du pancréas","synonyms":["Transformation kystique des acini pancréatiques","TKA pancréatique"]},"de":{"name":"Azinäre zystische Transformation des Pankreas","synonyms":["Azinuszell-Zystadenom des Pankreas","Pankreatische akinäre zystische Transformation"]},"es":{"name":"Transformación quística acinar del páncreas","synonyms":["Cistoadenoma de células acinares","Transformación quística acinar pancreática"]},"it":{"name":"Trasformazione cistica acinare del pancreas","synonyms":["Trasformazione cistica degli acini pancreatici","Cistadenoma a cellule acinari","Trasformazione cistica acinare del pancreas"]},"nl":{"name":"Acinaire cystische transformatie van pancreas","synonyms":["Acinaire cystische transformatie van alvleesklier","Acinuscelcystadenoom"]},"pt":{"name":"Acinar cystic transformation of the pancreas"},"pl":{"name":"Zrazikowo-torbielowata transformacja trzustki","synonyms":["Acinar cell cystadnoma","Pancreatic acinar cystic transformation"]},"cs":{"name":"Acinar cystic transformation of the pancreas","synonyms":["Acinar cell cystadnoma","Pancreatic acinar cystic transformation"]}},"xrefs":[{"source":"ICD-10","code":"D13.6","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2E92.8","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1664905891"}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97935,"name":"Rare gastroenterologic disease"},"parents":[{"orpha":101937,"name":"Rare pancreatic disease","classifications":[152]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adolescent","Adult","Childhood","Elderly"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":50.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}