raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:685004

Primary pericardial mesothelioma

Synonyms: PPM · Primary malignant pericardial mesothelioma

Type
Disease
Group
Disorder
Inheritance
Not applicable
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enPrimary pericardial mesotheliomaPPM · Primary malignant pericardial mesothelioma
frMésothéliome péricardique primitifMésothéliome péricardique malin primitif
dePerikardmesotheliom, primäresPPM · Primäres malignes Mesotheliom des Herzbeutels · Primäres perikardiales Mesotheliom
esMesotelioma pericárdico primarioMPP · Mesotelioma pericárdico maligno primario · Mesotelioma primario de pericardio
itMesotelioma pericardico primitivoPPM · Mesotelioma pericardico primitivo maligno
nlPrimair pericardiaal mesothelioomPPM · Primair maligne pericardiaal mesothelioom
ptMesotelioma pericárdico primárioMesotelioma maligno pericárdico primário · PPM
plPrimary pericardial mesothelioma= en
csPrimární mezoteliom perikardu= en
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-112C28.1NTBTindexvalidated
MONDO3805Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card