{"orpha":685004,"name":"Primary pericardial mesothelioma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["PPM","Primary malignant pericardial mesothelioma"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-685004/","orphanet_url":"https://www.orpha.net/en/disease/detail/685004","names":{"fr":{"name":"Mésothéliome péricardique primitif","synonyms":["Mésothéliome péricardique malin primitif"]},"de":{"name":"Perikardmesotheliom, primäres","synonyms":["PPM","Primäres malignes Mesotheliom des Herzbeutels","Primäres perikardiales Mesotheliom"]},"es":{"name":"Mesotelioma pericárdico primario","synonyms":["MPP","Mesotelioma pericárdico maligno primario","Mesotelioma primario de pericardio"]},"it":{"name":"Mesotelioma pericardico primitivo","synonyms":["PPM","Mesotelioma pericardico primitivo maligno"]},"nl":{"name":"Primair pericardiaal mesothelioom","synonyms":["PPM","Primair maligne pericardiaal mesothelioom"]},"pt":{"name":"Mesotelioma pericárdico primário","synonyms":["Mesotelioma maligno pericárdico primário","PPM"]},"pl":{"name":"Primary pericardial mesothelioma","synonyms":["PPM","Primary malignant pericardial mesothelioma"]},"cs":{"name":"Primární mezoteliom perikardu","synonyms":["PPM","Primary malignant pericardial mesothelioma"]}},"xrefs":[{"source":"ICD-11","code":"2C28.1","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1050817733"},{"source":"MONDO","code":"3805","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":168194,"name":"Rare cardiac tumor","classifications":[146,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}