raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:675404

May-Thurner syndrome

Synonyms: Cockett syndrome · MTS

Type
Disease
Group
Disorder
Inheritance
Not applicable
Status
active

A rare vascular disease characterized by venous insufficiency, obstruction or thrombosis usually caused by compression of the left common iliac vein between the right common iliac artery and the underlying spine with subsequent development of a left deep vein thrombosis (DVT). Patients may present with pain, swelling, venous stasis ulcers, skin pigmentation changes and post-thrombotic syndrome.

1

Names in Orphadata languages

10 of 12 languages
LangNameSynonyms
enMay-Thurner syndromeCockett syndrome · MTS
frSyndrome de May-ThurnerSyndrome de Cockett
deMay-Thurner-SyndromCockett-Syndrom · MTS
esSíndrome de May-ThurnerSíndrome de Cockett
itSindrome di May-ThurnerSMT · Sindrome di Cockett
nlSyndroom van May-ThurnerMTS · Syndroom van Cockett
ptSíndrome May-ThurnerMTS · Síndrome Cockett
plZespół May-Thurnera= en
csMay-Thurnerův syndromMayův-Thurnerův syndrom
ukСиндром Мей-ТернераСиндром Кокета · МТС

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10I87.1NTBTattributedvalidated
ICD-11BD73.2YNTBTattributedvalidated
MONDO0043361Evalidated
MONDO43361Evalidated
UMLSC3165062Evalidated
MedDRA10069727Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card