May-Thurner syndrome
Synonyms: Cockett syndrome · MTS
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Status
- active
A rare vascular disease characterized by venous insufficiency, obstruction or thrombosis usually caused by compression of the left common iliac vein between the right common iliac artery and the underlying spine with subsequent development of a left deep vein thrombosis (DVT). Patients may present with pain, swelling, venous stasis ulcers, skin pigmentation changes and post-thrombotic syndrome.
Names in Orphadata languages
10 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | May-Thurner syndrome | Cockett syndrome · MTS |
| fr | Syndrome de May-Thurner | Syndrome de Cockett |
| de | May-Thurner-Syndrom | Cockett-Syndrom · MTS |
| es | Síndrome de May-Thurner | Síndrome de Cockett |
| it | Sindrome di May-Thurner | SMT · Sindrome di Cockett |
| nl | Syndroom van May-Thurner | MTS · Syndroom van Cockett |
| pt | Síndrome May-Thurner | MTS · Síndrome Cockett |
| pl | Zespół May-Thurnera | = en |
| cs | May-Thurnerův syndrom | Mayův-Thurnerův syndrom |
| uk | Синдром Мей-Тернера | Синдром Кокета · МТС |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | I87.1 | NTBT | attributed | validated |
| ICD-11 | BD73.2Y | NTBT | attributed | validated |
| MONDO | 0043361 | E | validated | |
| MONDO | 43361 | E | validated | |
| UMLS | C3165062 | E | validated | |
| MedDRA | 10069727 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:496924Non-inflammatory vasculopathy
rare circulatory system diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/675404
- This record as JSON: /data/d/675404.json