ORPHA:674
Accessory pancreas
- Type
- Morphological anomaly
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Infancy, Neonatal
- Status
- active
A rare asymptomatic embryopathy characterized by the presence of pancreatic tissue in other sites of the body such as the splenic pedicle, gonadic pedicles, intestinal mesentery, duodenum wall, upper jejunum, or, more rarely, the gastric wall, ileum, gallbladder or spleen.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Accessory pancreas | |
| fr | Pancréas accessoire | |
| de | Pankreas, akzessorisches | |
| es | Páncreas accesorio | |
| it | Pancreas accessorio | |
| nl | Accessoire pancreas | Accessoire pancreas · Bijkomstige alvleesklier |
| pt | Pâncreas acessório | |
| pl | Śledziona dodatkowa | |
| cs | Akcesorní pankreas | |
| uk | Додаткова підшлункова залоза | |
| zh | 副胰 | |
| tr | Aksesuar pankreas |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | Q45.3 | NTBT | inclusion | validated |
| ICD-11 | LB21.2 | E | specific | validated |
| MONDO | 0019034 | E | validated | |
| MeSH | C536003 | E | validated | |
| UMLS | C0266268 | E | validated | |
| GARD | 454 | E | validated | |
| MedDRA | 10056987 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:108971Non-syndromic visceral malformation of the liver, biliary tract, pancreas or spleen
rare developmental anomalies during embryogenesis; rare genetic diseases; rare abdominal surgical diseases; rare transplant-related disorders
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | <1 / 1 000 000 | — | Europe | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/674
- This record as JSON: /data/d/674.json