{"orpha":674,"name":"Accessory pancreas","type":"Morphological anomaly","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"A rare asymptomatic embryopathy characterized by the presence of pancreatic tissue in other sites of the body such as the splenic pedicle, gonadic pedicles, intestinal mesentery, duodenum wall, upper jejunum, or, more rarely, the gastric wall, ileum, gallbladder or spleen.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-674/","orphanet_url":"https://www.orpha.net/en/disease/detail/674","names":{"fr":{"name":"Pancréas accessoire","definition":"Le pancréas accessoire est une embryopathie asymptomatique définie par la présence de tissu pancréatique au sein d'autres sites tels que le pédicule splénique, les pédicules gonadiques, le mésentère intestinal, la paroi du duodénum, la partie supérieure du jéjunum ou, plus rarement, la paroi gastrique, l'iléon, la vésicule biliaire ou la rate."},"de":{"name":"Pankreas, akzessorisches","definition":"Das akzessorische Pankreas ist eine symptomlose embryonale Entwicklungsstörung mit Pankreasgewebe an anderen Stellen des Körpers: Milzstiel, Gonadenstiele, Mesenterium, Duodenalwand und oberes Jejunum. Seltenere Lokalisationen sind: Magenwand, Ileum, Gallenblase oder Milz."},"es":{"name":"Páncreas accesorio","definition":"Es una embriopatía asintomática caracterizada por la presencia de tejido pancreático en otros lugares del organismo, como el pedículo esplénico, los pedículos gonádicos, el mesenterio intestinal, la pared del duodeno, el yeyuno superior o, más raramente, la pared gástrica, el íleo, la vesícula biliar o el bazo."},"it":{"name":"Pancreas accessorio"},"nl":{"name":"Accessoire pancreas","synonyms":["Accessoire pancreas","Bijkomstige alvleesklier"],"definition":"Een zeldzame, asymptomatische embryopathie, gekenmerkt door de aanwezigheid van pancreasweefsel in andere delen van het lichaam zoals pedikel van milt, pedikels van gonaden, intestinaal mesenterium, wand van duodenum, bovenste deel van jejunum, of, zeldzamer, maagwand, ileum, galblaas of milt."},"pt":{"name":"Pâncreas acessório"},"pl":{"name":"Śledziona dodatkowa"},"cs":{"name":"Akcesorní pankreas"},"uk":{"name":"Додаткова підшлункова залоза","definition":"A rare asymptomatic embryopathy characterized by the presence of pancreatic tissue in other sites of the body such as the splenic pedicle, gonadic pedicles, intestinal mesentery, duodenum wall, upper jejunum, or, more rarely, the gastric wall, ileum, gallbladder or spleen."},"zh":{"name":"副胰"},"tr":{"name":"Aksesuar pankreas"}},"xrefs":[{"source":"ICD-10","code":"Q45.3","qualifier":"NTBT","icd_relation":"inclusion","validated":true},{"source":"ICD-11","code":"LB21.2","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"240534435"},{"source":"MONDO","code":"0019034","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"C536003","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0266268","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"454","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10056987","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93890,"name":"Rare developmental defect during embryogenesis"},"parents":[{"orpha":108971,"name":"Non-syndromic visceral malformation of the liver, biliary tract, pancreas or spleen","classifications":[147,156,182,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Infancy","Neonatal"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Europe","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}