raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:673473

Borderline vascular tumor

Synonyms: Borderline vascular neoplasm · Vascular intermediate tumors · Vascular locally aggressive tumors

Type
Clinical group
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

10 of 12 languages
LangNameSynonyms
enBorderline vascular tumorBorderline vascular neoplasm · Vascular intermediate tumors · Vascular locally aggressive tumors
frTumeur vasculaire frontièreTumeur vasculaire de résécabilité limite · umeurs vasculaires à malignité intermédiaire ou incertaine
deBorderline-GefäßtumorVaskuläre Borderline-Neoplasie · Vaskulärer intermediärer Tumor · Vaskulärer lokal aggressiver Tumor
esTumor vascular limítrofeNeoplasia vascular limítrofe · Tumores vasculares intermedios · Tumores vasculares localmente agresivos
itTumore vascolare borderlineTumori intermedi · Tumori localmente aggressivi
nlVasculaire borderlinetumor'Borderline' vasculair neoplasma · 'Borderline' vasculaire tumor · Intermediaire vasculaire tumoren · Lokaal agressieve vasculaire tumoren · Vasculaire tumor met onzeker maligne potentieel
ptTumor vascular borderlineTumores vasculares intermédios · Neoplasia vascular borderline · Tumores vasculares agressivos localmente
plBorderline vascular tumor= en
csHraniční cévní nádor= en
ukПогранична судинна пухлинаПроміжні пухлини · Місцево-агресивні пухлини
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
UMLSC5925087Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (7):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card