ORPHA:673473
Borderline vascular tumor
Synonyms: Borderline vascular neoplasm · Vascular intermediate tumors · Vascular locally aggressive tumors
- Type
- Clinical group
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
1
Names in Orphadata languages
10 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Borderline vascular tumor | Borderline vascular neoplasm · Vascular intermediate tumors · Vascular locally aggressive tumors |
| fr | Tumeur vasculaire frontière | Tumeur vasculaire de résécabilité limite · umeurs vasculaires à malignité intermédiaire ou incertaine |
| de | Borderline-Gefäßtumor | Vaskuläre Borderline-Neoplasie · Vaskulärer intermediärer Tumor · Vaskulärer lokal aggressiver Tumor |
| es | Tumor vascular limítrofe | Neoplasia vascular limítrofe · Tumores vasculares intermedios · Tumores vasculares localmente agresivos |
| it | Tumore vascolare borderline | Tumori intermedi · Tumori localmente aggressivi |
| nl | Vasculaire borderlinetumor | 'Borderline' vasculair neoplasma · 'Borderline' vasculaire tumor · Intermediaire vasculaire tumoren · Lokaal agressieve vasculaire tumoren · Vasculaire tumor met onzeker maligne potentieel |
| pt | Tumor vascular borderline | Tumores vasculares intermédios · Neoplasia vascular borderline · Tumores vasculares agressivos localmente |
| pl | Borderline vascular tumor | = en |
| cs | Hraniční cévní nádor | = en |
| uk | Погранична судинна пухлина | Проміжні пухлини · Місцево-агресивні пухлини |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| UMLS | C5925087 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:211237Rare vascular tumor
rare developmental anomalies during embryogenesis; rare circulatory system diseases; rare neoplastic diseases
Children (7):
- ORPHA:458758Composite hemangioendothelioma
- ORPHA:33276Kaposi sarcoma
- ORPHA:2122Kaposiform hemangioendothelioma
- ORPHA:464321Multifocal lymphangioendotheliomatosis-thrombocytopenia syndrome
- ORPHA:458768Papillary intralymphatic angioendothelioma
- ORPHA:673556Pseudomyogenic hemangioendothelioma
- ORPHA:458763Retiform hemangioendothelioma
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/673473
- This record as JSON: /data/d/673473.json