{"orpha":673473,"name":"Borderline vascular tumor","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["Borderline vascular neoplasm","Vascular intermediate tumors","Vascular locally aggressive tumors"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-673473/","orphanet_url":"https://www.orpha.net/en/disease/detail/673473","names":{"fr":{"name":"Tumeur vasculaire frontière","synonyms":["Tumeur vasculaire de résécabilité limite","umeurs vasculaires à malignité intermédiaire ou incertaine"]},"de":{"name":"Borderline-Gefäßtumor","synonyms":["Vaskuläre Borderline-Neoplasie","Vaskulärer intermediärer Tumor","Vaskulärer lokal aggressiver Tumor"]},"es":{"name":"Tumor vascular limítrofe","synonyms":["Neoplasia vascular limítrofe","Tumores vasculares intermedios","Tumores vasculares localmente agresivos"]},"it":{"name":"Tumore vascolare borderline","synonyms":["Tumori intermedi","Tumori localmente aggressivi"]},"nl":{"name":"Vasculaire borderlinetumor","synonyms":["'Borderline' vasculair neoplasma","'Borderline' vasculaire tumor","Intermediaire vasculaire tumoren","Lokaal agressieve vasculaire tumoren","Vasculaire tumor met onzeker maligne potentieel"]},"pt":{"name":"Tumor vascular borderline","synonyms":["Tumores vasculares intermédios","Neoplasia vascular borderline","Tumores vasculares agressivos localmente"]},"pl":{"name":"Borderline vascular tumor","synonyms":["Borderline vascular neoplasm","Vascular intermediate tumors","Vascular locally aggressive tumors"]},"cs":{"name":"Hraniční cévní nádor","synonyms":["Borderline vascular neoplasm","Vascular intermediate tumors","Vascular locally aggressive tumors"]},"uk":{"name":"Погранична судинна пухлина","synonyms":["Проміжні пухлини","Місцево-агресивні пухлини"]}},"xrefs":[{"source":"UMLS","code":"C5925087","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98028,"name":"Rare circulatory system disease"},"parents":[{"orpha":211237,"name":"Rare vascular tumor","classifications":[147,198,202]}],"children":[{"orpha":458758,"name":"Composite hemangioendothelioma","type":"Disease"},{"orpha":33276,"name":"Kaposi sarcoma","type":"Disease"},{"orpha":2122,"name":"Kaposiform hemangioendothelioma","type":"Disease"},{"orpha":464321,"name":"Multifocal lymphangioendotheliomatosis-thrombocytopenia syndrome","type":"Disease"},{"orpha":458768,"name":"Papillary intralymphatic angioendothelioma","type":"Disease"},{"orpha":673556,"name":"Pseudomyogenic hemangioendothelioma","type":"Disease"},{"orpha":458763,"name":"Retiform hemangioendothelioma","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}