ORPHA:664901
Trigeminal trophic syndrome
Synonyms: TTS · Trigeminal neuropathy with nasal ulceration · Trigeminal neurotrophic ulceration · Trophic ulceration of the ala nasi
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
Orphadata ships no English definition for this code.
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Names in Orphadata languages
10 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Trigeminal trophic syndrome | TTS · Trigeminal neuropathy with nasal ulceration · Trigeminal neurotrophic ulceration · Trophic ulceration of the ala nasi |
| fr | Syndrome trophique trigéminal | Névralgie du trijumeau · STT · Syndrome trophique du trijumeau · Ulcération neurotrophique du trijumeau |
| de | Trigeminales trophisches Syndrom | Nasenflügelgeschwür, trophoneurotisches · Trigeminus-Syndrom, neurotrophes · Trigeminusneuropathie mit nasalem Ulkus · Trophisches Syndrom des N. trigeminus |
| es | Síndrome trófico trigeminal | Neuropatía del trigémino con ulceración nasal · Ulceración neurotrófica trigeminal · Ulceración trófica del ala nasal |
| it | Sindrome trofica del trigemino | Neuropatia del trigemino con ulcera del naso · STT · Ulcera neurotrofica del trigemino · Ulcera trofica delle ali del naso |
| nl | Trofisch syndroom van nervus trigeminus | Neuropathie van nervus trigeminus met nasale ulceratie · TTS · Trigeminale neurotrofe ulceratie · Trigeminus trofisch syndroom · Trofische ulceratie van ala nasi · Trofische ulceratie van neusvleugel |
| pt | Síndrome trófica do trigémio | Neuropatia do trigémio com ulceração nasal · TTS · Ulceração neurotrófica do trigémio · Ulceração trófica da ala nasi |
| pl | Zespół troficzny nerwu trójdzielnego | = en |
| cs | Trigeminální trofický syndrom | = en |
| uk | Трофічний синдром трійчастого нерва | Невропатія трійчастого нерва з виразкою в носі · Нейротрофічна виразка трійчастого нерва · Трофічна виразка піднебінної дужки · TTS |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | G50.8 | NTBT | attributed | validated |
| MONDO | 0800478 | E | validated | |
| MONDO | 800478 | E | validated | |
| UMLS | C1274928 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:221109Cranial neuralgia
rare neurological diseases - ORPHA:90077Other acquired skin disease
rare skin diseases
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Cases/families | 200 cases | Worldwide | Case(s) | Validated | 29931799[PMID] | |
| Point prevalence | <1 / 1 000 000 | — | Worldwide | Class only | Validated | 29931799[PMID]_ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/664901
- This record as JSON: /data/d/664901.json