raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:664901

Trigeminal trophic syndrome

Synonyms: TTS · Trigeminal neuropathy with nasal ulceration · Trigeminal neurotrophic ulceration · Trophic ulceration of the ala nasi

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult, Elderly
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

10 of 12 languages
LangNameSynonyms
enTrigeminal trophic syndromeTTS · Trigeminal neuropathy with nasal ulceration · Trigeminal neurotrophic ulceration · Trophic ulceration of the ala nasi
frSyndrome trophique trigéminalNévralgie du trijumeau · STT · Syndrome trophique du trijumeau · Ulcération neurotrophique du trijumeau
deTrigeminales trophisches SyndromNasenflügelgeschwür, trophoneurotisches · Trigeminus-Syndrom, neurotrophes · Trigeminusneuropathie mit nasalem Ulkus · Trophisches Syndrom des N. trigeminus
esSíndrome trófico trigeminalNeuropatía del trigémino con ulceración nasal · Ulceración neurotrófica trigeminal · Ulceración trófica del ala nasal
itSindrome trofica del trigeminoNeuropatia del trigemino con ulcera del naso · STT · Ulcera neurotrofica del trigemino · Ulcera trofica delle ali del naso
nlTrofisch syndroom van nervus trigeminusNeuropathie van nervus trigeminus met nasale ulceratie · TTS · Trigeminale neurotrofe ulceratie · Trigeminus trofisch syndroom · Trofische ulceratie van ala nasi · Trofische ulceratie van neusvleugel
ptSíndrome trófica do trigémioNeuropatia do trigémio com ulceração nasal · TTS · Ulceração neurotrófica do trigémio · Ulceração trófica da ala nasi
plZespół troficzny nerwu trójdzielnego= en
csTrigeminální trofický syndrom= en
ukТрофічний синдром трійчастого нерваНевропатія трійчастого нерва з виразкою в носі · Нейротрофічна виразка трійчастого нерва · Трофічна виразка піднебінної дужки · TTS
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10G50.8NTBTattributedvalidated
MONDO0800478Evalidated
MONDO800478Evalidated
UMLSC1274928Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

2 records
TypeClassValueAreaQualificationValidationSource
Cases/families200 casesWorldwideCase(s)Validated29931799[PMID]
Point prevalence<1 / 1 000 000—WorldwideClass onlyValidated29931799[PMID]_ORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card