{"orpha":664901,"name":"Trigeminal trophic syndrome","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["TTS","Trigeminal neuropathy with nasal ulceration","Trigeminal neurotrophic ulceration","Trophic ulceration of the ala nasi"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-664901/","orphanet_url":"https://www.orpha.net/en/disease/detail/664901","names":{"fr":{"name":"Syndrome trophique trigéminal","synonyms":["Névralgie du trijumeau","STT","Syndrome trophique du trijumeau","Ulcération neurotrophique du trijumeau"]},"de":{"name":"Trigeminales trophisches Syndrom","synonyms":["Nasenflügelgeschwür, trophoneurotisches","Trigeminus-Syndrom, neurotrophes","Trigeminusneuropathie mit nasalem Ulkus","Trophisches Syndrom des N. trigeminus"]},"es":{"name":"Síndrome trófico trigeminal","synonyms":["Neuropatía del trigémino con ulceración nasal","Ulceración neurotrófica trigeminal","Ulceración trófica del ala nasal"]},"it":{"name":"Sindrome trofica del trigemino","synonyms":["Neuropatia del trigemino con ulcera del naso","STT","Ulcera neurotrofica del trigemino","Ulcera trofica delle ali del naso"]},"nl":{"name":"Trofisch syndroom van nervus trigeminus","synonyms":["Neuropathie van nervus trigeminus met nasale ulceratie","TTS","Trigeminale neurotrofe ulceratie","Trigeminus trofisch syndroom","Trofische ulceratie van ala nasi","Trofische ulceratie van neusvleugel"]},"pt":{"name":"Síndrome trófica do trigémio","synonyms":["Neuropatia do trigémio com ulceração nasal","TTS","Ulceração neurotrófica do trigémio","Ulceração trófica da ala nasi"]},"pl":{"name":"Zespół troficzny nerwu trójdzielnego","synonyms":["TTS","Trigeminal neuropathy with nasal ulceration","Trigeminal neurotrophic ulceration","Trophic ulceration of the ala nasi"]},"cs":{"name":"Trigeminální trofický syndrom","synonyms":["TTS","Trigeminal neuropathy with nasal ulceration","Trigeminal neurotrophic ulceration","Trophic ulceration of the ala nasi"]},"uk":{"name":"Трофічний синдром трійчастого нерва","synonyms":["Невропатія трійчастого нерва з виразкою в носі","Нейротрофічна виразка трійчастого нерва","Трофічна виразка піднебінної дужки","TTS"]}},"xrefs":[{"source":"ICD-10","code":"G50.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0800478","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"800478","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1274928","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":221109,"name":"Cranial neuralgia","classifications":[181]},{"orpha":90077,"name":"Other acquired skin disease","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult","Elderly"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":200.0,"area":"Worldwide","status":"Validated","source":"29931799[PMID]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"29931799[PMID]_ORPHANET"}],"phenotypes":null}