ORPHA:658
Non-histaminic angioedema
Synonyms: Angioneurotic edema · Bradykinine-induced angioedema · Non histamine-induced angioedema
- Type
- Clinical group
- Group
- Group of disorders
- Inheritance
- Autosomal dominant, Not applicable
- Age of onset
- All ages
- Status
- active
A disorder that is characterized by the occurrence of transitory and recurrent subcutaneous and/or submucosal edemas resulting in swelling and/or abdominal pain.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Non-histaminic angioedema | Angioneurotic edema · Bradykinine-induced angioedema · Non histamine-induced angioedema |
| fr | Angio-oedème | Angio-oedème bradykinique · Angio-oedème non histaminique · OAN · Oedème angioneurotique |
| de | Angioödem, nicht-Histamin-vermitteltes | Angioödem, Bradykinin-induziertes · Nicht-Histamin-induziertes Angioödem · Ödem, angioneurotisches |
| es | Angioedema no histamínico | Angioedema inducido por bradiquinina · Angioedema no inducido por histamina · Edema angioneurótico |
| it | Angioedema non istaminico | Angioedema indotto dalla bradichinina · Angioedema non indotto dall'istamina · Edema angioneurotico |
| nl | Niet-histamine-geïnduceerd angio-oedeem | Angioneurotisch oedeem · Bradykinine-geïnduceerd angio-oedeem |
| pt | Angioedema não-histamínico | Angioedema |
| pl | Obrzęk naczynioruchowy niehistaminowy | Obrzęk naczynioruchowy · Obrzęk naczynioruchowy indukowany bradykininą · Obrzęk naczynioruchowy nieindukowany histaminą |
| cs | Non-histaminový angioedém | Angioneurotický edém · Bradykininem-indukovaný angioedém · Non-histaminem indukovaný angioedém |
| uk | Негістамінний ангіоневротичний набряк | Ангіоневротичний набряк · Ангіоневротичний набряк, спричинений брадикініном · Ангіоневротичний набряк, не викликаний гістаміном |
| zh | 非组胺源性血管性水肿 | 非组胺源性血管性水肿 |
| tr | Histaminik olmayan anjiyoödem | Anjiyonörotik ödem · Bradikininin neden olduğu anjiyoödem · Histamin kaynaklı olmayan anjiyoödem |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 0019013 | E | validated | |
| MONDO | 19013 | E | validated | |
| UMLS | C0002994 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:98004Rare immune disease
rare immunological diseases
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | 1-9 / 100 000 | — | Europe | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/658
- This record as JSON: /data/d/658.json