Idiopathic scleritis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Status
- active
A rare form of scleritis characterized by tender or painful, violet-blueish eye, with edema and injection of deep scleral vessels, in the absence of infection or systemic autoimmune diseases. It can be unilateral or bilateral. Other ocular signs depend on the localisation (anterior or posterior) and on the type of scleritis (diffuse, nodular or necrotizing). Extension to other layers of the eye and to peri-ocular tissues as well as visual impairment are potential complications. Idiopathic scleritis is more frequent in children than in adults.
Names in Orphadata languages
10 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Idiopathic scleritis | |
| fr | Sclérite idiopathique | |
| de | Skleritis, idiopathische | |
| es | Escleritis idiopática | |
| it | Sclerite idiopatica | |
| nl | Idiopathische scleritis | |
| pt | Esclerite idiopática | |
| pl | Idiopatyczne zapalenie twardówki | |
| cs | Idiopatická skleritida | |
| uk | Ідіопатичний склероз |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | H15.0 | NTBT | specific | validated |
| ICD-11 | 9B51 | NTBT | attributed | validated |
| MONDO | 0958265 | E | validated | |
| MONDO | 958265 | E | validated | |
| UMLS | C5816747 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:648559Rare scleritis
rare ophthalmic disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/648675
- This record as JSON: /data/d/648675.json