raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:64692

Bartonella bacilliformis infection

Synonyms: Bartonellosis due to infection with Bartonella bacilliformis · Carrion disease

Type
Disease
Group
Disorder
Age of onset
All ages
Status
active

A rare bacterial infectious disease transmitted between humans via bites from infected sand flies in high-altitude valleys of the South American Andes, characterized by two disparate syndromes which can arise independently or sequentially. The first, Oroya fever, occurs about 60 days after the fly bite as a severe hemorrhagic fever with high mortality in untreated individuals. The second, chronic phase, termed verruga peruana, can persist for months or years and manifests with endothelial cell-derived, blood-filled tumors developing on the surface of the skin.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enBartonella bacilliformis infectionBartonellosis due to infection with Bartonella bacilliformis · Carrion disease
frInfection à Bartonella bacilliformisBartonellose à Bartonella bacilliformis · Maladie de Carrion
deBartonella bacilliformis-InfektionBartonellose durch Infektion mit Bartonella bacilliformis · Carrión-Krankheit
esInfección por Bartonella bacilliformisBartonelosis por infección con Bartonella bacilliformis · Enfermedad de Carrion
itInfezione da Bartonella bacilliformisBartonellosi dovuta a infezione da Bartonella bacilliformis · Malattia di Carrion
nlInfectie door Bartonella bacilliformisBartonellose door infectie door Bartonella bacilliformis · Ziekte van Carrion
ptInfeção por Bartonella bacilliformisBartonelose por infeção por Bartonella bacilliformis · Doença Carrion
plGorączka OroyaBartonelloza spowodowana infekcją Bartonella bacilliformis · Choroba Carriona · Zakażenie Bartonella bacilliformis
csInfekce Bartonella bacilliformisCarriónova nemoc · Bartonelóza způsobená infekcí Bartonella bacilliformis
ukІнфекція Bartonella bacilliformisБартонельоз, спричинений паличкоподібною бартонелою (Bartonella bacilliformis) · Хвороба Карріона
zh奥罗亚热杆菌状巴尔通体感染所致巴尔通体病
trOroya ateşiCarrion hastalığı · Bartonella bacilliformis enfeksiyonuna bağlı bartonelloz

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10A44.0Especificvalidated
ICD-111C11.0Especificvalidated
MeSHD001474Evalidated
UMLSC4552012Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (2):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card