raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:639

Polyneuropathy associated with IgM monoclonal gammopathy with anti-MAG

inactive · moved to ORPHA:209004Polyneuropathy associated with IgM monoclonal gammopathy

Synonyms: Anti-MAG neuropathy · Neuropathy associated with monoclonal IgM antibodies to myelin-associated glycoprotein

Type
Disease
Group
Disorder
Status
inactive
Flag
Deprecated entity

This entity has been excluded from the Orphanet nomenclature of rare diseases and moved to Polyneuropathy associated with IgM monoclonal gammopathy

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPolyneuropathy associated with IgM monoclonal gammopathy with anti-MAGAnti-MAG neuropathy · Neuropathy associated with monoclonal IgM antibodies to myelin-associated glycoprotein
frPolyneuropathie associée à une gammopathie monoclonale IgM ayant une activité anti-MAGNeuropathie anti-MAG · Neuropathie associée à une IgM monoclonale anti-MAG · Neuropathie associée à une IgM monoclonale anti-glycoprotéine associée à la myéline
dePolyneuropathie mit monoklonaler IgM-Gammopathie mit Anti-MAGAnti-MAG-Neuropathie · Neuropathie mit assoziierten monoklonalen IgM-Antikörpern gegen Myelin-assoziiertes Glykoprotein
esPolineuropatía asociada a gammapatía monoclonal IgM con anti-MAGNeuropatía anti-MAG · Neuropatía asociada con anticuerpos monoclonales de IgM contra glicoproteína asociada a la mielina
itPolineuropatia associata a gammopatia monoclonale IgM con anti-MAGNeuropatia anti-MAG · Neuropatia associata ad anticorpi IgM monoclonali anti-glicoproteina associata alla mielina
nlPolyneuropathie geassocieerd met IgM monoklonale gammopathie met anti-MAGAnti-MAG-neuropathie · Neuropathie geassocieerd met monoklonale IgM-antilichamen tegen myelinegeassocieerd glycoproteïne
ptNeuropatia desmielinizante crónica com gamapatia IgM monoclonal
plPolineuropatia związana z gammapatią monoklonalną IgM z anty-MAGNeuropatia anty-MAG · Polineuropatia związana z gammapatią monoklonalną IgM z anty-MAG
csPolyneuropatie asociovaná s IgM monoklonální gamapatií s anti-MAGAnti-MAG neuropatie · Neuropatie asociovaná s monoklonálními protilátkami IgM proti glykoproteinu asociovanému s myelinem
ukПолінейропатія, асоційована з IgM моноклональною гаммапатією з анти-MAGАнти-MAG нейропатія · Нейропатія, асоційована з моноклональними IgM антитілами до мієлін-асоційованого глікопротеїну
zhMAG抗体阳性的IgM单克隆丙种球蛋白病伴相关性多发性神经病抗MAG神经病
trAnti-MAG ile seyreden IgM monoklonal gamopati -ilişkili polinöropatiMiyelin ilişkili glikoproteine karşı monoklonal IgM antikorları ile ilişkili nöropati · Anti-MAG nöropati

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO0018977Evalidated
UMLSC1736154Evalidated
MedDRA10078324Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card