raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:622099

Superior mesenteric artery syndrome

Synonyms: SMAS · Wilkie syndrome

Type
Disease
Group
Disorder
Inheritance
Not applicable
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

10 of 12 languages
LangNameSynonyms
enSuperior mesenteric artery syndromeSMAS · Wilkie syndrome
frSyndrome de l'artère mésentérique supérieureSyndrome de Wilkie
deSyndrom der oberen MesenterialarterieSMAS · Wilkie-Syndrom
esSíndrome de la arteria mesentérica superiorSAMS · Síndrome de Wilkie
itSindrome dell’arteria mesenterica superioreSMAS · Sindrome di Wilkie
nlArteria mesenterica superior-syndroomSyndroom van Wilkie · Grote darmslagader-syndroom · SMAS
ptSíndrome de artéria mesentérica superiorSMAS · Síndrome Wilkie
plZespół tętnicy krezkowej górnej= en
csSyndrom horní mezenterické tepny= en
ukСиндром верхньої брижової артеріїSMAS · Синдром Вілкі
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10K31.5NTBTattributedvalidated
ICD-11DA52.YNTBTindexvalidated
MONDO0002687Evalidated
MeSHD013478Evalidated
UMLSC0038828Evalidated
GARD7712Evalidated
MedDRA10054156Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card