ORPHA:622099
Superior mesenteric artery syndrome
Synonyms: SMAS · Wilkie syndrome
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Status
- active
Orphadata ships no English definition for this code.
1
Names in Orphadata languages
10 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Superior mesenteric artery syndrome | SMAS · Wilkie syndrome |
| fr | Syndrome de l'artère mésentérique supérieure | Syndrome de Wilkie |
| de | Syndrom der oberen Mesenterialarterie | SMAS · Wilkie-Syndrom |
| es | Síndrome de la arteria mesentérica superior | SAMS · Síndrome de Wilkie |
| it | Sindrome dellarteria mesenterica superiore | SMAS · Sindrome di Wilkie |
| nl | Arteria mesenterica superior-syndroom | Syndroom van Wilkie · Grote darmslagader-syndroom · SMAS |
| pt | Síndrome de artéria mesentérica superior | SMAS · Síndrome Wilkie |
| pl | Zespół tętnicy krezkowej górnej | = en |
| cs | Syndrom horní mezenterické tepny | = en |
| uk | Синдром верхньої брижової артерії | SMAS · Синдром Вілкі |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | K31.5 | NTBT | attributed | validated |
| ICD-11 | DA52.Y | NTBT | index | validated |
| MONDO | 0002687 | E | validated | |
| MeSH | D013478 | E | validated | |
| UMLS | C0038828 | E | validated | |
| GARD | 7712 | E | validated | |
| MedDRA | 10054156 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:165711Rare abdominal surgical disease
rare abdominal surgical diseases - ORPHA:117569Rare intestinal disease
rare gastroenterological diseases
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/622099
- This record as JSON: /data/d/622099.json