{"orpha":622099,"name":"Superior mesenteric artery syndrome","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["SMAS","Wilkie syndrome"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-622099/","orphanet_url":"https://www.orpha.net/en/disease/detail/622099","names":{"fr":{"name":"Syndrome de l'artère mésentérique supérieure","synonyms":["Syndrome de Wilkie"]},"de":{"name":"Syndrom der oberen Mesenterialarterie","synonyms":["SMAS","Wilkie-Syndrom"]},"es":{"name":"Síndrome de la arteria mesentérica superior","synonyms":["SAMS","Síndrome de Wilkie"]},"it":{"name":"Sindrome dellarteria mesenterica superiore","synonyms":["SMAS","Sindrome di Wilkie"]},"nl":{"name":"Arteria mesenterica superior-syndroom","synonyms":["Syndroom van Wilkie","Grote darmslagader-syndroom","SMAS"]},"pt":{"name":"Síndrome de artéria mesentérica superior","synonyms":["SMAS","Síndrome Wilkie"]},"pl":{"name":"Zespół tętnicy krezkowej górnej","synonyms":["SMAS","Wilkie syndrome"]},"cs":{"name":"Syndrom horní mezenterické tepny","synonyms":["SMAS","Wilkie syndrome"]},"uk":{"name":"Синдром верхньої брижової артерії","synonyms":["SMAS","Синдром Вілкі"]}},"xrefs":[{"source":"ICD-10","code":"K31.5","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"DA52.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"389867507"},{"source":"MONDO","code":"0002687","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D013478","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0038828","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"7712","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10054156","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97935,"name":"Rare gastroenterologic disease"},"parents":[{"orpha":165711,"name":"Rare abdominal surgical disease","classifications":[182]},{"orpha":117569,"name":"Rare intestinal disease","classifications":[152]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}