Amniotic fluid embolism
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A rare obstetric condition characterized by entry of amniotic fluid and fetal elements into the maternal circulation, causing an emergency situation with sudden cardiovascular collapse, disseminated intravascular coagulation, and high lethality. In most instances it occurs during labor, cesarean delivery, or within 30 minutes postpartum. Patients present acute dyspnea and cough, acute hypotension, encephalopathy with altered mental status and seizures, hypoxia and cyanosis, coagulopathy, severe hemorrhage, uterine atony, acute pulmonary hypertension, and cardiac arrest.
Names in Orphadata languages
10 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Amniotic fluid embolism | |
| fr | Embolie de liquide amniotique | |
| de | Fruchtwasserembolie | |
| es | Embolia de líquido amniótico | |
| it | Embolia del liquido amniotico | |
| nl | Vruchtwaterembolie | |
| pt | Embolia de líquido amniótico | |
| pl | Zator płynem owodniowym | |
| cs | Embolie plodovou vodou | |
| uk | Емболія навколоплідними водами |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | O88.1 | E | specific | validated |
| ICD-11 | JB42.1 | E | specific | validated |
| MONDO | 0850046 | E | validated | |
| MeSH | D004619 | E | validated | |
| UMLS | C0013927 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:163637Rare disorder related with pregnancy, childbirth and puerperium
rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | United Kingdom | Class only | Validated | 31714909[PMID]_ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/617304
- This record as JSON: /data/d/617304.json