ORPHA:60026
Pulmonary nodular lymphoid hyperplasia
Synonyms: Pulmonary pseudolymphoma
- Type
- Disease
- Group
- Disorder
- Age of onset
- Adolescent, Adult, Childhood
- Status
- active
Pulmonary nodular lymphoid hyperplasia (PNHL) is a reactive lymphoid proliferation manifesting as solitary or multiple nodules in the lung.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Pulmonary nodular lymphoid hyperplasia | Pulmonary pseudolymphoma |
| fr | Hyperplasie lymphoïde nodulaire pulmonaire | Pseudolymphome du poumon |
| de | Hyperplasie, lymphoide pulmonale noduläre | Pseudolymphom, pulmonales |
| es | Hiperplasia linfoide nodular y pulmonar | Pseudolinfoma pulmonar |
| it | Iperplasia linfatica nodulare polmonare | Pseudolinfoma polmonare |
| nl | Pulmonale nodulaire lymfoïdhyperplasie | Pulmonaal pseudolymfoom |
| pt | Hiperplasia linfóide nodular pulmonar | Pseudo-linfoma pulmonar |
| pl | Guzkowy rozrost limfoidalny płuc | Pseudochłoniak płuc |
| cs | Plicní nodulární lymfoidní hyperplázie | Plicní pseudolymfom |
| uk | Вузлова лімфоїдна гіперплазія легень | Псевдолімфома легень |
| zh | 肺假性淋巴瘤 | 肺假性淋巴瘤 |
| tr | Pulmoner nodüler lenfoid hiperplazi | Pulmoner psödolenfoma |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| OMIM | 178610 | E | validated | |
| ICD-10 | J98.4 | NTBT | attributed | validated |
| ICD-11 | CB40.Y | NTBT | attributed | validated |
| MONDO | 0008348 | E | validated | |
| UMLS | C1334969 | E | validated | |
| MedDRA | 10077412 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:101944Rare pulmonary disease
rare respiratory diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
10 annotations · validated 2021-01-20| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Frequent (79-30%) | ||
| HP:0012735 | Cough | |
| HP:0002729 | Follicular hyperplasia | |
| HP:0100721 | Mediastinal lymphadenopathy | |
| HP:0025392 | Nodular pattern on pulmonary HRCT | |
| HP:0030150 | Plasmacytosis | |
| Occasional (29-5%) | ||
| HP:0100749 | Chest pain | |
| HP:0002094 | Dyspnea | |
| HP:0025179 | Ground-glass opacification on pulmonary HRCT | |
| Very rare (<4-1%) | ||
| HP:0030057 | Autoimmune antibody positivity | |
| HP:0002721 | Immunodeficiency | |
Annotation source: 29902913[PMID]_30720334[PMID]_28609772[PMID]
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/60026
- This record as JSON: /data/d/60026.json