raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:592873

Acute transverse myelitis with anti-MOG antibodies

Synonyms: Acute transverse myelitis with anti-myelin oligodendrocyte glycoprotein antibodies

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
Adolescent, Adult, Childhood, Elderly, Infancy
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enAcute transverse myelitis with anti-MOG antibodiesAcute transverse myelitis with anti-myelin oligodendrocyte glycoprotein antibodies
frMyélite transverse aiguë avec anticorps anti-MOG
deAkute transverse Myelitis mit anti-MOG-AntikörperMyelitis, akute transverse, mit anti-Myelin-Oligodendrozyten-Glykoprotein-Antikörper
esMielitis transversa aguda con anticuerpos anti-MOGMielitis transversa aguda con anticuerpos anti-glicoproteína mielínica oligodendrocitaria
itMielite trasversa acuta con anticorpi anti-MOGMielite trasversa acuta con anticorpi anti-glicoproteina mielinica oligodendrocitaria
nlAcute transversale myelitis met anti-MOG antilichamenAcute transversale myelitis met anti-myeline oligodendrocyt glycoproteïne antilichamen
ptMielite transversa aguda com anticorpos anti-MOGMielite transversa aguda com anticorpos anti-glicoproteína mielínica oligodendrocitária
plOstre poprzeczne zapalenie rdzenia z przeciwciałami przeciw glikoproteinie oligodendrocytów mielinyOstre poprzeczne zapalenie rdzenia z przeciwciałami przeciw MOG
csAkutní transverzální myelitida s anti-MOG protilátkami= en
ukГострий поперечний мієліт з анти-MOG антитіламиГострий поперечний мієліт з антитілами до глікопротеїну олігодендроцитів проти мієліну
zhAcute transverse myelitis with anti-MOG antibodies= en
trAcute transverse myelitis with anti-MOG antibodies= en
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10G37.3NTBTspecificvalidated
MONDO0035666Evalidated
UMLSC5680298Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

2 records
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET
Annual incidenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card