ORPHA:570438
HHV-8-associated multicentric Castleman disease
Synonyms: Human herpesvirus-8-associated multicentric Castleman disease
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
Orphadata ships no English definition for this code.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | HHV-8-associated multicentric Castleman disease | Human herpesvirus-8-associated multicentric Castleman disease |
| fr | Maladie de Castleman multicentrique associée à HHV-8 | Maladie de Castleman multicentrique associée à l'herpèsvirus humain 8 |
| de | Castleman-Krankheit, multizentrische, HHV-8-assoziierte | Humane Herpesvirus 8-assoziierte multizentrische Castleman-Krankheit |
| es | Enfermedad de Castleman multicéntrica asociada a HHV-8 | Enfermedad de Castleman multicéntrica asociada a virus herpes humano-8 |
| it | Malattia di Castleman multicentrica associata a HHV-8 | Malattia di Castleman multicentrica associata al virus herpes umano 8 |
| nl | HHV-8-geassocieerde multicentrische ziekte van Castleman | Humaan herpesvirus 8-geassocieerde multicentrische ziekte van Castleman |
| pt | Doença Castleman multicêntrica HHV-8 associada | |
| pl | Choroba Castelmana multicentryczna związana z HHV-8 | = en |
| cs | Multicentrická Castlemanova choroba spojená s HHV-8 | = en |
| uk | HHV-8-асоційована мультицентрична хвороба Каслмана | Герпесвірус-8, асоційована мультицентрична хвороба Каслмана |
| zh | HHV-8相关的多中心卡斯特莱曼病 | 人类疱疹病毒-8相关的多中心卡斯特莱曼病 |
| tr | HHV-8 -ilişkili multisentrik Castleman hastalığı | İnsan herpes virüsü-8-ilişkili multisentrik Castleman hastalığı |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D47.7 | NTBT | attributed | validated |
| ICD-11 | 2A81.Y | NTBT | index | validated |
| ICD-11 | XH5HJ5 | E | specific | validated |
| MONDO | 0019754 | E | validated | |
| UMLS | C5197664 | E | validated | |
| GARD | 22310 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:160Castleman disease
rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders - ORPHA:102024Human herpesvirus 8-related disorder
rare neoplastic diseases
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/570438
- This record as JSON: /data/d/570438.json