{"orpha":570438,"name":"HHV-8-associated multicentric Castleman disease","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Human herpesvirus-8-associated multicentric Castleman disease"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-570438/","orphanet_url":"https://www.orpha.net/en/disease/detail/570438","names":{"fr":{"name":"Maladie de Castleman multicentrique associée à HHV-8","synonyms":["Maladie de Castleman multicentrique associée à l'herpèsvirus humain 8"]},"de":{"name":"Castleman-Krankheit, multizentrische, HHV-8-assoziierte","synonyms":["Humane Herpesvirus 8-assoziierte multizentrische Castleman-Krankheit"]},"es":{"name":"Enfermedad de Castleman multicéntrica asociada a HHV-8","synonyms":["Enfermedad de Castleman multicéntrica asociada a virus herpes humano-8"]},"it":{"name":"Malattia di Castleman multicentrica associata a HHV-8","synonyms":["Malattia di Castleman multicentrica associata al virus herpes umano 8"]},"nl":{"name":"HHV-8-geassocieerde multicentrische ziekte van Castleman","synonyms":["Humaan herpesvirus 8-geassocieerde multicentrische ziekte van Castleman"]},"pt":{"name":"Doença Castleman multicêntrica HHV-8 associada"},"pl":{"name":"Choroba Castelmana multicentryczna związana z HHV-8","synonyms":["Human herpesvirus-8-associated multicentric Castleman disease"]},"cs":{"name":"Multicentrická Castlemanova choroba spojená s HHV-8","synonyms":["Human herpesvirus-8-associated multicentric Castleman disease"]},"uk":{"name":"HHV-8-асоційована мультицентрична хвороба Каслмана","synonyms":["Герпесвірус-8, асоційована мультицентрична хвороба Каслмана"]},"zh":{"name":"HHV-8相关的多中心卡斯特莱曼病","synonyms":["人类疱疹病毒-8相关的多中心卡斯特莱曼病"]},"tr":{"name":"HHV-8 -ilişkili multisentrik Castleman hastalığı","synonyms":["İnsan herpes virüsü-8-ilişkili multisentrik Castleman hastalığı"]}},"xrefs":[{"source":"ICD-10","code":"D47.7","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2A81.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"890839710"},{"source":"ICD-11","code":"XH5HJ5","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1581356165"},{"source":"MONDO","code":"0019754","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5197664","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"22310","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97992,"name":"Rare hematologic disease"},"parents":[{"orpha":160,"name":"Castleman disease","classifications":[194,202,233]},{"orpha":102024,"name":"Human herpesvirus 8-related disorder","classifications":[202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}