ORPHA:570431
Idiopathic multicentric Castleman disease
Synonyms: HHV-8-negative multicentric Castleman disease · Human herpesvirus-8-negative multicentric Castleman disease
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
Orphadata ships no English definition for this code.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Idiopathic multicentric Castleman disease | HHV-8-negative multicentric Castleman disease · Human herpesvirus-8-negative multicentric Castleman disease |
| fr | Maladie de Castleman multicentrique idiopathique | Maladie de Castleman multicentrique non associée à HHV-8 · Maladie de Castleman multicentrique non associée à l'herpèsvirus humain 8 |
| de | Castleman-Krankheit, multizentrische, idiopathische | HHV-8-negative multizentrische Castleman-Krankheit · Humane Herpesvirus 8-negative multizentrische Castleman-Krankheit |
| es | Enfermedad de Castleman multicéntrica idiopática | Enfermedad de Castleman multicéntrica HHV-8 negativo · Enfermedad de Castleman multicéntrica virus herpes humano-8 negativo |
| it | Malattia di Castleman multicentrica idiopatica | Malattia di Castleman multicentrica negativa a HHV-8 · Malattia di Castleman multicentrica negativa al virus herpes umano 8 |
| nl | Idiopathische multicentrische ziekte van Castleman | HHV-8-negatieve multicentrische ziekte van Castleman · Humaan herpesvirus 8-negatieve multicentrische ziekte van Castleman |
| pt | Doença Castleman multicêntrica idiopática | |
| pl | Idiopatyczna choroba Castelmana multicentryczna | = en |
| cs | Idiopatická multicentrická Castlemanova choroba | = en |
| uk | Ідіопатична мультицентрична хвороба Каслмана | HHV-8-негативна мультицентрична хвороба Каслмана · Герпесвірус людини 8-негативна мультицентрична хвороба Каслмана |
| zh | 特发性多中心卡斯特莱曼病 | 人类疱疹病毒-8阴性多中心卡斯特莱曼病 |
| tr | İdiyopatik multisentrik Castleman hastalığı | HHV-8-negatif multisentrik Castleman hastalığı · İnsan herpes virüsü-8-negatif multisentrik Castleman hastalığı |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D47.7 | NTBT | attributed | validated |
| ICD-11 | 4B2Y | NTBT | attributed | validated |
| MONDO | 0035838 | E | validated | |
| UMLS | C5197665 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:160Castleman disease
rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET_29157611[PMID] |
| Annual incidence | 1-9 / 1 000 000 | — | United States | Class only | Validated | ORPHANET_25120049[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/570431
- This record as JSON: /data/d/570431.json