{"orpha":570431,"name":"Idiopathic multicentric Castleman disease","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["HHV-8-negative multicentric Castleman disease","Human herpesvirus-8-negative multicentric Castleman disease"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-570431/","orphanet_url":"https://www.orpha.net/en/disease/detail/570431","names":{"fr":{"name":"Maladie de Castleman multicentrique idiopathique","synonyms":["Maladie de Castleman multicentrique non associée à HHV-8","Maladie de Castleman multicentrique non associée à l'herpèsvirus humain 8"]},"de":{"name":"Castleman-Krankheit, multizentrische, idiopathische","synonyms":["HHV-8-negative multizentrische Castleman-Krankheit","Humane Herpesvirus 8-negative multizentrische Castleman-Krankheit"]},"es":{"name":"Enfermedad de Castleman multicéntrica idiopática","synonyms":["Enfermedad de Castleman multicéntrica HHV-8 negativo","Enfermedad de Castleman multicéntrica virus herpes humano-8 negativo"]},"it":{"name":"Malattia di Castleman multicentrica idiopatica","synonyms":["Malattia di Castleman multicentrica negativa a HHV-8","Malattia di Castleman multicentrica negativa al virus herpes umano 8"]},"nl":{"name":"Idiopathische multicentrische ziekte van Castleman","synonyms":["HHV-8-negatieve multicentrische ziekte van Castleman","Humaan herpesvirus 8-negatieve multicentrische ziekte van Castleman"]},"pt":{"name":"Doença Castleman multicêntrica idiopática"},"pl":{"name":"Idiopatyczna choroba Castelmana multicentryczna","synonyms":["HHV-8-negative multicentric Castleman disease","Human herpesvirus-8-negative multicentric Castleman disease"]},"cs":{"name":"Idiopatická multicentrická Castlemanova choroba","synonyms":["HHV-8-negative multicentric Castleman disease","Human herpesvirus-8-negative multicentric Castleman disease"]},"uk":{"name":"Ідіопатична мультицентрична хвороба Каслмана","synonyms":["HHV-8-негативна мультицентрична хвороба Каслмана","Герпесвірус людини 8-негативна мультицентрична хвороба Каслмана"]},"zh":{"name":"特发性多中心卡斯特莱曼病","synonyms":["人类疱疹病毒-8阴性多中心卡斯特莱曼病"]},"tr":{"name":"İdiyopatik multisentrik Castleman hastalığı","synonyms":["HHV-8-negatif multisentrik Castleman hastalığı","İnsan herpes virüsü-8-negatif multisentrik Castleman hastalığı"]}},"xrefs":[{"source":"ICD-10","code":"D47.7","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"4B2Y","qualifier":"NTBT","icd_relation":"attributed","validated":true,"icd11_uri":"null"},{"source":"MONDO","code":"0035838","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5197665","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97992,"name":"Rare hematologic disease"},"parents":[{"orpha":160,"name":"Castleman disease","classifications":[194,202,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET_29157611[PMID]"},{"type":"Annual incidence","qualification":"Class only","class":"1-9 / 1 000 000","value":0.0,"area":"United States","status":"Validated","source":"ORPHANET_25120049[PMID]"}],"phenotypes":null}