ORPHA:567552
Idiopathic steroid-resistant nephrotic syndrome with sensitivity to second-line immunosuppressive therapy
Synonyms: Idiopathic steroid-resistant nephrotic syndrome with sensitivity to intensified immunosuppression
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
Orphadata ships no English definition for this code.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Idiopathic steroid-resistant nephrotic syndrome with sensitivity to second-line immunosuppressive therapy | Idiopathic steroid-resistant nephrotic syndrome with sensitivity to intensified immunosuppression |
| fr | Syndrome néphrotique corticorésistant idiopathique avec sensibilité à l'immunosuppression intensive | SNCR idiopathique avec sensibilité à l'immunosuppression intensive · Syndrome néphrotique corticorésistant idiopathique avec sensibilité aux traitements immunosuppresseurs de deuxième intention |
| de | Idiopathisches steroid-resistentes nephrotisches Syndrom mit Sensitivität zu immunsuppressiver Zweitlinien-Therapie | Idiopathisches steroid-resistentes nephrotisches Syndrom mit Empfindlichkeit gegenüber verstärkter Immunsuppression |
| es | Síndrome nefrótico idiopático resistente a esteroides con sensibilidad a terapia inmunosupresora de segunda línea | Síndrome nefrótico idiopático resistente a esteroides con sensibilidad a la inmunosupresión intensificada |
| it | Sindrome nefrosica idiopatica resistente agli steroidi sensibile alla terapia immunosoppressiva di seconda linea | Sindrome nefrosica idiopatica resistente agli steroidi sensibile alla terapia immunosoppressiva intensificata |
| nl | Idiopathisch steroïdresistent nefrotisch syndroom met sensitiviteit voor immuunsuppressieve tweedelijnsbehandeling | Idiopathisch steroïdresistent nefrotisch syndroom met sensitiviteit voor geïntensiveerde immuunsuppressie |
| pt | Síndrome nefrótica cortico-resistente idiopática com sensibilidade a terapêutica imunosupressora de segunda linha | Síndrome nefrótica corticorresistente idiopática com sensibilidade a terapêutica imunosupressora intensiva |
| pl | Idiopatyczny zespół nerczycowy oporny na sterydy z nadwrażliwością na terapię immunospupresyjną drugiego rzutu | = en |
| cs | Idiopatický nefrotický syndrom rezistentní na steroidy s citlivostí na imunosupresivní léčbu druhé linie | = en |
| uk | Ідіопатичний стероїдорезистентний нефротичний синдром з чутливістю до імуносупресивної терапії другої лінії | Ідіопатичний стероїдорезистентний нефротичний синдром з чутливістю до посиленої імуносупресії |
| zh | 对二线免疫抑制治疗敏感的特发性类固醇抵抗肾病综合征 | 对强化免疫抑制治疗敏感的特发性类固醇抵抗肾病综合征 |
| tr | İkinci basamak immünosüpresif tedaviye duyarlılık ile seyreden idiyopatik steroide dirençli nefrotik sendrom | İdiopatik steroide dirençli nefrotik sendrom, yoğunlaştırılmış immünosupresyona duyarlılık |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | N04.8 | NTBT | attributed | validated |
| MONDO | 0035460 | E | validated | |
| UMLS | C5680133 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:567548Idiopathic steroid-resistant nephrotic syndrome
rare renal diseases; rare transplant-related disorders
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/567552
- This record as JSON: /data/d/567552.json