{"orpha":567552,"name":"Idiopathic steroid-resistant nephrotic syndrome with sensitivity to second-line immunosuppressive therapy","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Idiopathic steroid-resistant nephrotic syndrome with sensitivity to intensified immunosuppression"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-567552/","orphanet_url":"https://www.orpha.net/en/disease/detail/567552","names":{"fr":{"name":"Syndrome néphrotique corticorésistant idiopathique avec sensibilité à l'immunosuppression intensive","synonyms":["SNCR idiopathique avec sensibilité à l'immunosuppression intensive","Syndrome néphrotique corticorésistant idiopathique avec sensibilité aux traitements immunosuppresseurs de deuxième intention"]},"de":{"name":"Idiopathisches steroid-resistentes nephrotisches Syndrom mit Sensitivität zu immunsuppressiver Zweitlinien-Therapie","synonyms":["Idiopathisches steroid-resistentes nephrotisches Syndrom mit Empfindlichkeit gegenüber verstärkter Immunsuppression"]},"es":{"name":"Síndrome nefrótico idiopático resistente a esteroides con sensibilidad a terapia inmunosupresora de segunda línea","synonyms":["Síndrome nefrótico idiopático resistente a esteroides con sensibilidad a la inmunosupresión intensificada"]},"it":{"name":"Sindrome nefrosica idiopatica resistente agli steroidi sensibile alla terapia immunosoppressiva di seconda linea","synonyms":["Sindrome nefrosica idiopatica resistente agli steroidi sensibile alla terapia immunosoppressiva intensificata"]},"nl":{"name":"Idiopathisch steroïdresistent nefrotisch syndroom met sensitiviteit voor immuunsuppressieve tweedelijnsbehandeling","synonyms":["Idiopathisch steroïdresistent nefrotisch syndroom met sensitiviteit voor geïntensiveerde immuunsuppressie"]},"pt":{"name":"Síndrome nefrótica cortico-resistente idiopática com sensibilidade a terapêutica imunosupressora de segunda linha","synonyms":["Síndrome nefrótica corticorresistente idiopática com sensibilidade a terapêutica imunosupressora intensiva"]},"pl":{"name":"Idiopatyczny zespół nerczycowy oporny na sterydy z nadwrażliwością na terapię immunospupresyjną drugiego rzutu","synonyms":["Idiopathic steroid-resistant nephrotic syndrome with sensitivity to intensified immunosuppression"]},"cs":{"name":"Idiopatický nefrotický syndrom rezistentní na steroidy s citlivostí na imunosupresivní léčbu druhé linie","synonyms":["Idiopathic steroid-resistant nephrotic syndrome with sensitivity to intensified immunosuppression"]},"uk":{"name":"Ідіопатичний стероїдорезистентний нефротичний синдром з чутливістю до імуносупресивної терапії другої лінії","synonyms":["Ідіопатичний стероїдорезистентний нефротичний синдром з чутливістю до посиленої імуносупресії"]},"zh":{"name":"对二线免疫抑制治疗敏感的特发性类固醇抵抗肾病综合征","synonyms":["对强化免疫抑制治疗敏感的特发性类固醇抵抗肾病综合征"]},"tr":{"name":"İkinci basamak immünosüpresif tedaviye duyarlılık ile seyreden idiyopatik steroide dirençli nefrotik sendrom","synonyms":["İdiopatik steroide dirençli nefrotik sendrom, yoğunlaştırılmış immünosupresyona duyarlılık"]}},"xrefs":[{"source":"ICD-10","code":"N04.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0035460","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680133","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93626,"name":"Rare renal disease"},"parents":[{"orpha":567548,"name":"Idiopathic steroid-resistant nephrotic syndrome","classifications":[188,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[],"phenotypes":null}