raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:567550

Idiopathic multidrug-resistant nephrotic syndrome

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
All ages
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enIdiopathic multidrug-resistant nephrotic syndrome
frSyndrome néphrotique idiopathique avec résistance multiple aux médicaments
deIdiopathisches MDR-resistentes nephrotisches Syndrom
esSíndrome nefrótico idiopático resistente a múltiples fármacos
itSindrome nefrosica idiopatica multifarmaco-resistente
nlIdiopathisch multidrugresistent nefrotisch syndroom
ptSíndrome nefrótico multiresistente a fármacos idiopático
plIdiopatyczny zespół nerczycowy oporny na leki
csIdiopatický multirezistentní nefrotický syndrom
ukІдіопатичний мультирезистентний нефротичний синдром
zh特发性耐多药肾病综合征
trİdiyopatik çoklu ilaca dirençli nefrotik sendrom
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10N04.8NTBTattributedvalidated
MONDO0035459Evalidated
UMLSC5681293Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card