{"orpha":567550,"name":"Idiopathic multidrug-resistant nephrotic syndrome","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":[],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-567550/","orphanet_url":"https://www.orpha.net/en/disease/detail/567550","names":{"fr":{"name":"Syndrome néphrotique idiopathique avec résistance multiple aux médicaments"},"de":{"name":"Idiopathisches MDR-resistentes nephrotisches Syndrom"},"es":{"name":"Síndrome nefrótico idiopático resistente a múltiples fármacos"},"it":{"name":"Sindrome nefrosica idiopatica multifarmaco-resistente"},"nl":{"name":"Idiopathisch multidrugresistent nefrotisch syndroom"},"pt":{"name":"Síndrome nefrótico multiresistente a fármacos idiopático"},"pl":{"name":"Idiopatyczny zespół nerczycowy oporny na leki"},"cs":{"name":"Idiopatický multirezistentní nefrotický syndrom"},"uk":{"name":"Ідіопатичний мультирезистентний нефротичний синдром"},"zh":{"name":"特发性耐多药肾病综合征"},"tr":{"name":"İdiyopatik çoklu ilaca dirençli nefrotik sendrom"}},"xrefs":[{"source":"ICD-10","code":"N04.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0035459","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5681293","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93626,"name":"Rare renal disease"},"parents":[{"orpha":567548,"name":"Idiopathic steroid-resistant nephrotic syndrome","classifications":[188,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}