ORPHA:541
Primary cutaneous CD30+ T-cell lymphoproliferative disease
Synonyms: Primary cutaneous Ki-1+ T-cell lymphoproliferative disease
- Type
- Clinical group
- Group
- Group of disorders
- Age of onset
- Adult
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary cutaneous CD30+ T-cell lymphoproliferative disease | Primary cutaneous Ki-1+ T-cell lymphoproliferative disease |
| fr | Lymphoprolifération T cutanée primitive CD30+ | Lymphoprolifération T cutanée primitive Ki-1+ |
| de | Primär kutane CD30-positive T-Zell-Lymphoproliferation | Primär kutane Ki-1+ T-Zell-lymphoproliferative Krankheit |
| es | Enfermedad linfoproliferativa cutánea primaria de células T CD30+ | Enfermedad linfoproliferativa cutánea primaria de células T Ki-1+ |
| it | Malattia linfoproliferativa cutanea primitiva a cellule T CD30+ | Malattia linfoproliferativa cutanea primitiva a cellule T Ki-1+ |
| nl | Primaire cutane CD30+ T-cel lymfoproliferatieve ziekte | Primaire cutane Ki-1+ T-cel lymfoproliferatieve ziekte |
| pt | Linfoma de células grandes anaplásicas | Linfoma de células Ki1 |
| pl | Pierwotna skórna choroba limfoproliferacyjna z komórek T CD30+ | Pierwotna skórna choroba limfoproliferacyjna z komórek Ki-1+ T |
| cs | Primární kutánní CD30+ T-buněčná lymfoproliferativní nemoc | Primární kutánní Ki-1+ T-buněčná lymfoproliferativní nemoc |
| uk | Первинна шкірна CD30+ Т-клітинна лімфопроліферативна хвороба | Первинне шкірне Кі-1+ Т-клітинне лімфопроліферативне захворювання |
| zh | 原发性皮肤CD30+T细胞淋巴组织增生异常 | 原发性皮肤Ki-1+ T细胞淋巴组织增生性疾病 |
| tr | Primer kutanöz CD30 + T hücreli lenfoproliferatif hastalık | Primer kutanöz Ki-1 + T hücreli lenfoproliferatif hastalık |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C86.6 | E | specific | validated |
| ICD-11 | 2B03 | E | specific | validated |
| MONDO | 0018897 | E | validated | |
| MONDO | 18897 | E | validated | |
| UMLS | C5679826 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:178548Indolent primary cutaneous T-cell lymphoma
rare skin diseases; rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 1 000 000 | 0.18 / 100 000 | Europe | Value and class | Validated | OTHERitut de Veille Sanitaire 1990[OTHER] |
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/541
- This record as JSON: /data/d/541.json