{"orpha":541,"name":"Primary cutaneous CD30+ T-cell lymphoproliferative disease","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["Primary cutaneous Ki-1+ T-cell lymphoproliferative disease"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-541/","orphanet_url":"https://www.orpha.net/en/disease/detail/541","names":{"fr":{"name":"Lymphoprolifération T cutanée primitive CD30+","synonyms":["Lymphoprolifération T cutanée primitive Ki-1+"]},"de":{"name":"Primär kutane CD30-positive T-Zell-Lymphoproliferation","synonyms":["Primär kutane Ki-1+ T-Zell-lymphoproliferative Krankheit"]},"es":{"name":"Enfermedad linfoproliferativa cutánea primaria de células T CD30+","synonyms":["Enfermedad linfoproliferativa cutánea primaria de células T Ki-1+"]},"it":{"name":"Malattia linfoproliferativa cutanea primitiva a cellule T CD30+","synonyms":["Malattia linfoproliferativa cutanea primitiva a cellule T Ki-1+"]},"nl":{"name":"Primaire cutane CD30+ T-cel lymfoproliferatieve ziekte","synonyms":["Primaire cutane Ki-1+ T-cel lymfoproliferatieve ziekte"]},"pt":{"name":"Linfoma de células grandes anaplásicas","synonyms":["Linfoma de células Ki1"]},"pl":{"name":"Pierwotna skórna choroba limfoproliferacyjna z komórek T CD30+","synonyms":["Pierwotna skórna choroba limfoproliferacyjna z komórek Ki-1+ T"]},"cs":{"name":"Primární kutánní CD30+ T-buněčná lymfoproliferativní nemoc","synonyms":["Primární kutánní Ki-1+ T-buněčná lymfoproliferativní nemoc"]},"uk":{"name":"Первинна шкірна CD30+ Т-клітинна лімфопроліферативна хвороба","synonyms":["Первинне шкірне Кі-1+ Т-клітинне лімфопроліферативне захворювання"]},"zh":{"name":"原发性皮肤CD30+T细胞淋巴组织增生异常","synonyms":["原发性皮肤Ki-1+ T细胞淋巴组织增生性疾病"]},"tr":{"name":"Primer kutanöz CD30 + T hücreli lenfoproliferatif hastalık","synonyms":["Primer kutanöz Ki-1 + T hücreli lenfoproliferatif hastalık"]}},"xrefs":[{"source":"ICD-10","code":"C86.6","qualifier":"E","icd_relation":"specific","validated":true},{"source":"ICD-11","code":"2B03","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1046496266"},{"source":"MONDO","code":"0018897","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"18897","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5679826","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":178548,"name":"Indolent primary cutaneous T-cell lymphoma","classifications":[187,194,202,233]}],"children":[{"orpha":98842,"name":"Lymphomatoid papulosis","type":"Disease"},{"orpha":300865,"name":"Primary cutaneous anaplastic large cell lymphoma","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult"],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.18,"area":"Europe","status":"Validated","source":"OTHERitut de Veille Sanitaire 1990[OTHER]"},{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}