Lichen planopilaris
Synonyms: Follicular lichen planus · LPP · Lichen follicularis · Lichen planus follicularis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A rare cutaneous variant of lichen planus which affects hair follicles. It may occur on its own or in association with more common forms of lichen planus, usually classical type and/or oral lichen planus.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Lichen planopilaris | Follicular lichen planus · LPP · Lichen follicularis · Lichen planus follicularis |
| fr | Lichen plan pilaire | LPP · Lichen plan folliculaire |
| de | Lichen planopilaris | LPP · Lichen follicularis · Lichen planus follicularis · Lichen planus, follikulärer |
| es | Liquen plano pilar | Liquen folicular plano · Liquen plano pilaris · Liquen folicular |
| it | Lichen planus pilare | LPP · Lichen follicolare · Lichen planus follicolare · Lichen planus follicularis |
| nl | Lichen planopilaris | Folliculaire lichen planus · LPP · Lichen follicularis · Lichen planus follicularis |
| pt | Líquen plano folicular | |
| pl | Liszaj płaski mieszkowy | LPP |
| cs | Lichen planopilaris | Folikulární lichen planus · LPP · Lichen follicularis · Lichen planus follicularis |
| uk | Лишай плоский (Lichen planopilaris) | Фолікулярний плоский лишай · Фолікулярний лишай (Lichen follicularis) · Плоский лишай фолікулярний · LPP |
| zh | 毛囊扁平苔癣 | 毛发扁平苔藓 |
| tr | Liken planopilar | LPP · Liken follikülaris · Folliküler liken planus · Liken planus follikülaris |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | L66.1 | E | specific | validated |
| ICD-11 | EA91.2 | NTBT | index | validated |
| MONDO | 0018879 | E | validated | |
| MeSH | C535892 | E | validated | |
| UMLS | C0023645 | E | validated | |
| GARD | 3247 | E | validated | |
| MedDRA | 10081142 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:79364Alopecia
rare skin diseases - ORPHA:254370Rare cutaneous lichen planus
rare skin diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Cases/families | 300 cases | Worldwide | Case(s) | Validated | ORPHANET | |
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
15 annotations · validated 2016-06-01| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Very frequent (99-80%) | ||
| HP:0001596 | Alopecia | |
| HP:0000962 | Hyperkeratosis | |
| HP:0100725 | Lichenification | |
| HP:0200034 | Papule | |
| Frequent (79-30%) | ||
| HP:0001231 | Abnormal fingernail morphology | |
| HP:0004334 | Dermal atrophy | |
| HP:0000989 | Pruritus | |
| HP:0200042 | Skin ulcer | |
| Occasional (29-5%) | ||
| HP:0008066 | Abnormal blistering of the skin | |
| HP:0002242 | Abnormal intestine morphology | |
| HP:0012115 | Hepatitis | |
| HP:0001053 | Hypopigmented skin patches | |
| HP:0100649 | Neoplasm of the oral cavity | |
| HP:0001806 | Onycholysis | |
| HP:0001059 | Pterygium | |
Run the differential on the 4 obligate / very frequent terms
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/525
- This record as JSON: /data/d/525.json