ORPHA:51890

Anterior cutaneous nerve entrapment syndrome

Synonyms: ACNES · Intercostal nerve syndrome · Rectus abdominis syndrome

Type: Disease
Group: Disorder
Inheritance: Not applicable
Age of onset: All ages
Status: active

A chronic neuropathic pain syndrome of the abdominal wall caused by entrapment of anterior cutaneous branches of 7 to 12th intercostal nerves along the lateral border of the anterior rectus abdominis fascia causing severe pain and tenderness of the involved dermatome.

Names in Orphadata languages

12 of 12 languages

Lang	Name	Synonyms
en	Anterior cutaneous nerve entrapment syndrome	ACNES · Intercostal nerve syndrome · Rectus abdominis syndrome
fr	Syndrome rectus abdominis	ACNES · Syndrome du nerf intercostal
de	Kómár-Syndrom	Intercostalnerven-Syndrom · Rectus abdominis-Syndrom
es	Síndrome de atrapamiento del nervio cutáneo anterior	Síndrome de Komar
it	Sindrome da intrappolamento del nervo cutaneo anteriore	Sindrome del muscolo retto dell'addome · Sindrome del nervo intercostale
nl	Syndroom van Kómár	ACNES · Abdominale intercostale neuralgie · Beklemming van de anterieure tak van een intercostale zenuw · Buikwandpijnsyndroom · Intercostale zenuw-syndroom · Rectus abdominis-syndroom
pt	Síndrome de Komar	Síndrome dos nervos intercostais · Síndrome rectos abdominais
pl	Zespół Komara	Zespół mięśnia prostego brzucha · Zespół nerwu międzyżebrowego
cs	Entrapment syndrom předních větví kožních nervů	ACNES · Rectus abdominis syndrome · Intercostal nerve syndrome
uk	Синдром защемлення переднього шкірного нерва	ACNES · Синдром міжреберного нерва · Синдром прямих мязів живота
zh	前皮神经卡压综合征	肋间神经综合症
tr	Anterior kutanöz sinir tuzak sendromu	ACNES · Rektus abdominis sendromu · İnterkostal sinir sendromu

Definition in:

Cross-references

qualifier = Orphanet mapping relation

Source	Code	Qualifier	ICD relation	Validation
ICD-10	G58.0	NTBT	attributed	validated
ICD-11	8E43.Y	NTBT	index	validated
MONDO	0018873	E		validated
UMLS	C0393899	E		validated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

Classification

Preferential parent (Orphanet linearisation):

ORPHA:98006Rare neurologic disease

Parents in the classifications (1):

ORPHA:182086Acquired peripheral neuropathy
rare neurological diseases

No children.

Genes

0 direct

Orphanet records no gene directly on this code.

Prevalence and incidence

2 records

Type	Class	Value	Area	Qualification	Validation	Source
Point prevalence	Unknown	—	Worldwide	Class only	Not yet validated	ORPHANET
Annual incidence	6-9 / 10 000	55.6 / 100 000	Netherlands	Value and class	Validated	[EXPERT]_25887961[PMID]_72957[PMID]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

HPO phenotypes

17 annotations · validated 2019-11-06

HPO	Term (as annotated by Orphanet)	Diagnostic
Very frequent (99-80%)
HP:0002027	Abdominal pain
HP:0010830	Impaired tactile sensation
HP:0003474	Somatic sensory dysfunction
Frequent (79-30%)
HP:0000975	Hyperhidrosis
HP:0002321	Vertigo
Occasional (29-5%)
HP:0003270	Abdominal distention
HP:0012533	Allodynia
HP:0002039	Anorexia
HP:0003418	Back pain
HP:0003565	Elevated erythrocyte sedimentation rate
HP:0100963	Hyperesthesia
HP:0001974	Increased total leukocyte count
HP:0002018	Nausea
Very rare (<4-1%)
HP:0004325	Decreased body weight
HP:0000023	Inguinal hernia
HP:0004798	Recurrent infection of the gastrointestinal tract
HP:0000010	Recurrent urinary tract infections

Run the differential on the 3 obligate / very frequent terms

Annotation source: 24197667[PMID]_30817351[PMID]_29270882[PMID]_29516161[PMID]

Sources for this card

Orphanet page: orpha.net/en/disease/detail/51890
This record as JSON: /data/d/51890.json