ORPHA:48435
Postinfectious vasculitis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
Vasculitis, characterized by inflammatory lesions in the wall of vessels, may be due to different viruses.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Postinfectious vasculitis | |
| fr | Vascularite post-infectieuse | |
| de | Vaskulitis, postinfektiöse | |
| es | Vasculitis postinfecciosa | |
| it | Vasculite post-infettiva | |
| nl | Postinfectieuze vasculitis | |
| pt | Vasculite vírica não HBV não HCV | |
| pl | Poinfekcyjne zapalenie naczyń | |
| cs | Postinfekční vaskulitida | |
| uk | Постінфекційний васкуліт | |
| zh | 感染后血管炎 | |
| tr | Postinfeksiyöz vaskülit |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | I77.6 | NTBT | attributed | validated |
| ICD-11 | 4A44.Y | NTBT | attributed | validated |
| MONDO | 0018837 | E | validated | |
| UMLS | C4510302 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:102005Brain inflammatory disease
rare neurological diseases - ORPHA:445197Secondary vasculitis
rare systemic and rheumatological diseases; rare circulatory system diseases; rare systemic or rheumatologic diseases of childhood
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
57 annotations · validated 2021-09-07| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Frequent (79-30%) | ||
| HP:0010876 | Abnormal circulating protein level | |
| HP:0005368 | Abnormality of humoral immunity | |
| HP:0410008 | Abnormality of the peripheral nervous system | |
| HP:0002039 | Anorexia | |
| HP:0002829 | Arthralgia | |
| HP:0011227 | Elevated circulating C-reactive protein concentration | |
| HP:0001945 | Fever | |
| HP:0000099 | Glomerulonephritis | |
| HP:0012649 | Increased inflammatory response | |
| HP:0011123 | Inflammatory abnormality of the skin | |
| HP:0032018 | Multiple mononeuropathy | |
| HP:0003326 | Myalgia | |
| HP:0030166 | Night sweats | |
| HP:0031691 | Severe viral infection | |
| HP:0200029 | Vasculitis in the skin | |
| HP:0001824 | Weight loss | |
| Occasional (29-5%) | ||
| HP:0002027 | Abdominal pain | |
| HP:0001063 | Acrocyanosis | |
| HP:0003493 | Antinuclear antibody positivity | |
| HP:0001369 | Arthritis | |
| HP:0006689 | Bacterial endocarditis | |
| HP:0001638 | Cardiomyopathy | |
| HP:0005318 | Cerebral vasculitis | |
| HP:0025143 | Chills | |
| HP:0100778 | Cryoglobulinemia | |
| HP:0000965 | Cutis marmorata | |
| HP:0032230 | Cytoplasmic antineutrophil antibody positivity | |
| HP:0002617 | Dilatation | |
| HP:0020180 | Elevated haptoglobin level | |
| HP:0004386 | Gastrointestinal inflammation | |
| HP:0000790 | Hematuria | |
| HP:0000822 | Hypertension | |
| HP:0003261 | Increased circulating IgA level | |
| HP:0010702 | Increased circulating immunoglobulin concentration | |
| HP:0020101 | Invasive fungal infection | |
| HP:0002140 | Ischemic stroke | |
| HP:0000793 | Membranoproliferative glomerulonephritis | |
| HP:0002011 | Morphological central nervous system abnormality | |
| HP:0100796 | Orchitis | |
| HP:0031363 | Palpable purpura | |
| HP:0009830 | Peripheral neuropathy | |
| HP:0020114 | Persistent human papillomavirus infection | |
| HP:0002090 | Pneumonia | |
| HP:0000093 | Proteinuria | |
| HP:0030880 | Raynaud phenomenon | |
| HP:0002726 | Recurrent Staphylococcus aureus infections | |
| HP:0005401 | Recurrent candida infections | |
| HP:0011274 | Recurrent mycobacterial infections | |
| HP:0005366 | Recurrent streptococcus pneumoniae infections | |
| HP:0025188 | Retinal vasculitis | |
| HP:0002923 | Rheumatoid factor positive | |
| HP:0031693 | Severe Epstein Barr virus infection | |
| HP:0031692 | Severe cytomegalovirus infection | |
| HP:0032170 | Severe varicella zoster infection | |
| HP:0001482 | Subcutaneous nodule | |
| HP:0032166 | Unusual gastrointestinal infection | |
| HP:0006562 | Viral hepatitis | |
Annotation source: 25876145[PMID]_32348521[PMID]_29624865[PMID]
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/48435
- This record as JSON: /data/d/48435.json