{"orpha":48435,"name":"Postinfectious vasculitis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"Vasculitis, characterized by inflammatory lesions in the wall of vessels, may be due to different viruses.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-48435/","orphanet_url":"https://www.orpha.net/en/disease/detail/48435","names":{"fr":{"name":"Vascularite post-infectieuse","definition":"Différents virus peuvent être à l'origine des vascularites qui sont définies par l'existence d'une inflammation de la paroi vasculaire."},"de":{"name":"Vaskulitis, postinfektiöse","definition":"Eine Vaskulitis, charakterisiert durch entzündliche Läsionen der Gefäßwand, kann durch verschiedene Viren verursacht werden."},"es":{"name":"Vasculitis postinfecciosa","definition":"Es una vasculitis, caracterizada por lesiones inflamatorias en la pared de los vasos sanguíneos, que puede deberse a diferentes virus."},"it":{"name":"Vasculite post-infettiva"},"nl":{"name":"Postinfectieuze vasculitis","definition":"Vasculitis, gekenmerkt door inflammatoire laesies in bloedvatwanden, kan veroorzaakt worden door verschillende virussen."},"pt":{"name":"Vasculite vírica não HBV não HCV"},"pl":{"name":"Poinfekcyjne zapalenie naczyń"},"cs":{"name":"Postinfekční vaskulitida"},"uk":{"name":"Постінфекційний васкуліт","definition":"Vasculitis, characterized by inflammatory lesions in the wall of vessels, may be due to different viruses."},"zh":{"name":"感染后血管炎"},"tr":{"name":"Postinfeksiyöz vaskülit"}},"xrefs":[{"source":"ICD-10","code":"I77.6","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"4A44.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0018837","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4510302","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":102005,"name":"Brain inflammatory disease","classifications":[181]},{"orpha":445197,"name":"Secondary vasculitis","classifications":[196,198,231]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":{"validation_status":"y","online":"y","validation_date":"2021-09-07","source":"25876145[PMID]_32348521[PMID]_29624865[PMID]","terms":[{"hpo":"HP:0010876","label":"Abnormal circulating protein level","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0005368","label":"Abnormality of humoral immunity","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0410008","label":"Abnormality of the peripheral nervous system","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0002039","label":"Anorexia","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0002829","label":"Arthralgia","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0011227","label":"Elevated circulating C-reactive protein concentration","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0001945","label":"Fever","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0000099","label":"Glomerulonephritis","frequency":"Frequent 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(29-5%)","criteria":null},{"hpo":"HP:0020180","label":"Elevated haptoglobin level","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0004386","label":"Gastrointestinal inflammation","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0000790","label":"Hematuria","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0000822","label":"Hypertension","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0003261","label":"Increased circulating IgA level","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0010702","label":"Increased circulating immunoglobulin concentration","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0020101","label":"Invasive fungal infection","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0002140","label":"Ischemic stroke","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0000793","label":"Membranoproliferative glomerulonephritis","frequency":"Occasional 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