Idiopathic neonatal atrial flutter
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Infancy, Neonatal
- Status
- active
Idiopathic neonatal atrial flutter (AFL) is a rare rhythm disorder, characterized by sustained tachycardia in newborns and infants with an atrial rate often at around 440 beats/minute (range 340-580). AFL may manifest as asymptomatic tachycardia, congestive heart failure or hydrops.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Idiopathic neonatal atrial flutter | |
| fr | Flutter auriculaire idiopathique du nouveau-né | |
| de | Vorhofflattern, idiopathisches neonatales | |
| es | Flutter auricular neonatal idiopático | Aleteo atrial idiopático neonatal |
| it | Flutter atriale idiopatico neonatale | |
| nl | Idiopathische neonatale atriumflutter | Idiopathisch neonataal boezemfladderen |
| pt | Flutter auricular neonatal idiopático | |
| pl | Idiopatyczne niemowlęce trzepotanie przedsionków | |
| cs | Idiopatický novorozenecký síňový flutter | |
| uk | Ідіопатичне тріпотіння передсердь у новонароджених | |
| zh | 特发性新生儿房扑 | |
| tr | Yenidoğanın idiyopatik atriyal flutter |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | P29.1 | NTBT | attributed | validated |
| ICD-11 | BC81.20 | NTBT | index | validated |
| MONDO | 0018684 | E | validated | |
| UMLS | C4275090 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:218439Non-genetic cardiac rhythm disease
rare cardiac diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
3 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Prevalence at birth | 1-9 / 100 000 | 1.5 / 100 000 | Europe | Value and class | Validated | [EXPERT]_23551862[PMID] |
| Prevalence at birth | 1-9 / 100 000 | 2.1 / 100 000 | United Kingdom | Value and class | Validated | 23551862[PMID] |
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
15 annotations · validated 2021-01-14| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Very frequent (99-80%) | ||
| HP:0003115 | Abnormal EKG | |
| HP:0005150 | Abnormal atrioventricular conduction | |
| HP:0011675 | Arrhythmia | |
| HP:0004755 | Supraventricular tachycardia | |
| Frequent (79-30%) | ||
| HP:0025074 | Abnormal QRS complex | |
| HP:0005162 | Abnormal left ventricular function | |
| HP:0004763 | Paroxysmal supraventricular tachycardia | |
| HP:0012664 | Reduced left ventricular ejection fraction | |
| HP:0002789 | Tachypnea | |
| Occasional (29-5%) | ||
| HP:0008872 | Feeding difficulties in infancy | |
| HP:0025116 | Fetal distress | |
| HP:0001789 | Hydrops fetalis | |
| HP:0001520 | Large for gestational age | |
| HP:0009800 | Maternal diabetes | |
| HP:0002098 | Respiratory distress | |
Run the differential on the 4 obligate / very frequent terms
Annotation source: 29706767 [PMID]_263874[PMID]_9616850[PMID]_30511544[PMID]_32366806[PMID]
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/45452
- This record as JSON: /data/d/45452.json