Cutaneous pseudolymphoma
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
A rare acquired skin disease characterized by a benign, etiologically variable lymphoproliferative process of the skin mimicking cutaneous lymphoma clinically and/or histologically, while not fulfilling criteria for the diagnosis of a specific disease. Depending on the predominant cell type in the infiltrate, T- and B-cell pseudolymphomas can be distinguished.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Cutaneous pseudolymphoma | |
| fr | Pseudolymphome cutané | |
| de | Kutanes Pseudolymphom | |
| es | Pseudolinfoma cutáneo | |
| it | Pseudolinfoma cutaneo | |
| nl | Cutaan pseudolymfoom | |
| pt | Pseudolinfoma cutâneo | |
| pl | Pseudochłoniak skóry | |
| cs | Kožní pseudolymfomy | |
| uk | Шкірна псевдолімфома | |
| zh | 皮肤假性淋巴瘤 | |
| tr | Kutanöz psödolenfoma |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | L98.8 | NTBT | attributed | validated |
| ICD-11 | 4A43.0 | NTBT | index | validated |
| MONDO | 0018680 | E | validated | |
| UMLS | C0311220 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:284264IgG4-related disease
rare systemic and rheumatological diseases - ORPHA:90077Other acquired skin disease
rare skin diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | <1 / 1 000 000 | — | Worldwide | Class only | Validated | ORPHANET_27057027[PMID] |
| Cases/families | 60 cases | Worldwide | Case(s) | Validated | 27057027[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/451607
- This record as JSON: /data/d/451607.json